Department of Radiology, State Key Laboratory of Complex Severe and Rare Disease, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, 100730, China.
National Center for Quality Control of Radiology, Beijing, China.
BMC Urol. 2024 Aug 22;24(1):176. doi: 10.1186/s12894-024-01566-w.
Cellular angiofibroma is a rare benign mesenchymal tumor that mostly occurs in the genital area. Its occurrence outside this region, particularly in the pelvis, is extremely rare. To our knowledge, this study reports the first case of cellular angiofibroma occurring in the pelvic cavity, except for one case reported in the retroperitoneum.
A 25-year-old female patient with chronic, intermittent, dull pain in the lower abdomen that lasted for several months was referred to our clinic. Imaging studies revealed a tumor in the pelvic cavity anterior to the bladder. The radiographic characteristics of this tumor indicated a hypervascular nature, suggesting the possibility of a pheochromocytoma or a neuroendocrine tumor. The patient underwent surgical excision of the lesion. To date, no recurrence has been observed four months after excision.
Cellular angiofibroma, although rare in the pelvic cavity, should be considered in the differential diagnosis of hypervascular pelvic space-occupying lesions. Immunohistochemical staining can help confirm the diagnosis of this condition. Treatment is generally straightforward, involving local excision of the tumor followed by postoperative monitoring.
细胞性血管纤维瘤是一种罕见的良性间叶组织肿瘤,主要发生在生殖器区域。其在该区域以外的部位发生,特别是在骨盆内,极为罕见。据我们所知,本研究报告了首例发生在盆腔内的细胞性血管纤维瘤病例,除了 1 例发生在腹膜后。
一名 25 岁女性患者因慢性、间歇性、下腹钝痛数月就诊于我院。影像学检查显示盆腔内膀胱前有一个肿瘤。该肿瘤的影像学特征提示为富血管性,提示可能为嗜铬细胞瘤或神经内分泌肿瘤。患者接受了病变的手术切除。目前,切除后四个月未见复发。
细胞性血管纤维瘤虽然在盆腔内罕见,但在鉴别诊断富血管性盆腔占位性病变时应考虑到。免疫组织化学染色有助于明确该疾病的诊断。治疗通常很简单,包括肿瘤的局部切除,然后术后监测。