中年及老年期新诊断的囊性纤维化
Newly diagnosed cystic fibrosis in middle and later life.
作者信息
Hunt B, Geddes D M
出版信息
Thorax. 1985 Jan;40(1):23-6. doi: 10.1136/thx.40.1.23.
Abstract
Four patients with cystic fibrosis diagnosed in middle and later life are presented. All had chronic bronchopulmonary infection with a high sweat sodium concentration, and chest radiographic evidence of upper zone bronchiectasis. Two patients had pancreatic dysfunction. Sputum culture grew mucoid Pseudomonas aeruginosa in three patients and Haemophilus influenzae in one. Ages at diagnosis were 63, 42, 40, and 35 years. These patients confirm the possibility of occasional longevity in cystic fibrosis and emphasise the need to consider the diagnosis at all ages. They also provide encouragement for younger patients.
摘要
本文介绍了4例在中年及老年期被诊断为囊性纤维化的患者。所有患者均有慢性支气管肺部感染，汗液钠浓度升高，胸部X线显示上叶支气管扩张。2例患者有胰腺功能障碍。3例患者的痰培养生长出黏液型铜绿假单胞菌，1例生长出流感嗜血杆菌。诊断时的年龄分别为63岁、42岁、40岁和35岁。这些患者证实了囊性纤维化患者偶尔可长寿的可能性，并强调了在各个年龄段都需考虑该诊断的必要性。它们也为年轻患者带来了鼓舞。
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