Shanholtzer Andrew, Sidhom Daniel A, Suson Kristina D, Anderson Barrett G
Detroit Medical Center, Department of Urology, Detroit, MI, USA.
Children's Hospital of Michigan, Department of Urology, Detroit, MI, USA.
Urol Case Rep. 2024 Aug 3;56:102818. doi: 10.1016/j.eucr.2024.102818. eCollection 2024 Sep.
Zinner Syndrome (ZS) is a rare congenital genitourinary abnormality defined by seminal vesicle cysts, ejaculatory duct obstruction, and unilateral renal dysplasia or agenesis. Patients can be asymptomatic, while others experience pain, urinary or ejaculatory symptoms and infertility. A patient that presented with painless gross hematuria was found to have a large pelvic cystic structure, an absent left kidney, multiple fluid collections in the region of the left seminal vesicle and right hydronephrosis. Hydronephrosis is atypical in ZS. This patient eventually developed right flank and pelvic pain treated with robotic-assisted laparoscopic excision of the pelvic cystic structure and extravesical ureteral reimplantation.
齐纳综合征（ZS）是一种罕见的先天性泌尿生殖系统异常，其特征为精囊囊肿、射精管梗阻以及单侧肾发育不全或肾缺如。患者可能无症状，而其他患者则会出现疼痛、泌尿或射精症状以及不育。一名出现无痛性肉眼血尿的患者被发现有一个大的盆腔囊性结构、左肾缺如、左精囊区域有多个液性聚集以及右肾积水。肾积水在齐纳综合征中并不典型。该患者最终出现右胁腹和盆腔疼痛，接受了机器人辅助腹腔镜切除盆腔囊性结构及膀胱外输尿管再植术治疗。
