Division of Endocrinology, University of Florida Health, Jacksonville, FL, USA.
Division of Critical Care Medicine, Mayo Clinic, Jacksonville, FL, USA.
Am J Case Rep. 2024 Sep 8;25:e944024. doi: 10.12659/AJCR.944024.
BACKGROUND Pheochromocytoma, a rare catecholamine-secreting tumor, often presents with paroxysmal or sustained hypertension, tachycardia, headache, and diaphoresis. Timely diagnosis is essential to prevent adverse complications. Less common presentations include pheochromocytoma crisis, with severe neurological and cardiac complications. CASE REPORT We report a unique case of a 25-year-old woman who initially presented with pheochromocytoma-induced hypertensive encephalopathy and acute coronary syndrome. Echocardiography revealed takotsubo-like cardiomyopathy, and magnetic resonance imaging of the brain revealed posterior reversible encephalopathy syndrome. Initial treatment focused on controlling her blood pressure and supporting cardiac function. Due to her recovering from immediate crisis and absence of further symptoms, the patient refused further follow-up. However, she eventually experienced another episode of hypertensive crisis 2 years later. Subsequent investigations with 24-h urine tests revealed elevated vanillylmandelic acid levels (7.93 mg/24 h), normetanephrine (2638.72 µg/24 h), and nor-metanephrine to creatinine ratio (3546.67) and normal urine metanephrine levels (195.92 µg/24 h) and metanephrine to creatinine ratio (263.33). Contrast-enhanced computed tomography of the abdomen revealed a 4.3×3.1×4-cm mass in the right adrenal gland. A DOTATATE positron emission tomography scan revealed a 3.9×4.3×2.7-cm localized right adrenal pheochromocytoma. Biochemical testing and adrenal imaging revealed a previously undiagnosed pheochromocytoma. Following targeted medical therapy and right adrenalectomy, the patient achieved complete resolution of her hypertension and associated symptoms. CONCLUSIONS Our case is a unique simultaneous presentation of posterior reversible encephalopathy syndrome and takotsubo-like cardiomyopathy, highlighting the importance to consider pheochromocytoma in acute neurological and cardiac presentations, even in the absence of typical symptoms.
嗜铬细胞瘤是一种罕见的儿茶酚胺分泌肿瘤,常表现为阵发性或持续性高血压、心动过速、头痛和出汗。及时诊断对于预防不良并发症至关重要。不常见的表现包括嗜铬细胞瘤危象,伴有严重的神经和心脏并发症。
我们报告了一例 25 岁女性的独特病例,她最初表现为嗜铬细胞瘤引起的高血压性脑病和急性冠状动脉综合征。超声心动图显示类心尖球囊样心肌病,脑部磁共振成像显示后部可逆性脑病综合征。初始治疗侧重于控制血压和支持心脏功能。由于她从即刻危机中恢复,且没有出现进一步的症状,患者拒绝进一步随访。然而,她最终在 2 年后再次经历了一次高血压危象。随后的 24 小时尿液检查显示香草扁桃酸水平升高(7.93mg/24h),间甲肾上腺素(2638.72µg/24h)和间甲肾上腺素与肌酐比值(3546.67),尿液间甲肾上腺素水平正常(195.92µg/24h)和间甲肾上腺素与肌酐比值(263.33)。腹部增强计算机断层扫描显示右侧肾上腺有一个 4.3×3.1×4cm 的肿块。DOTATATE 正电子发射断层扫描显示右侧肾上腺有一个 3.9×4.3×2.7cm 的局限性嗜铬细胞瘤。生化检查和肾上腺成像显示出以前未诊断出的嗜铬细胞瘤。在进行靶向药物治疗和右侧肾上腺切除术之后,患者的高血压和相关症状完全缓解。
我们的病例是后部可逆性脑病综合征和类心尖球囊样心肌病同时出现的独特表现,强调了即使没有典型症状,在急性神经和心脏表现中也要考虑嗜铬细胞瘤的重要性。