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持续性室性心动过速:慢性嗜酸性粒细胞白血病的一种非典型表现。

Incessant Ventricular Tachycardia: An Atypical Presentation of Chronic Eosinophilic Leukemia.

作者信息

Takla Andrew, Shah Purva, Sbenghe Maria, Baibhav Bipul, Feitell Scott

机构信息

Department of Internal Medicine, Rochester General Hospital, Rochester, New York, USA.

Department of Hematology and Oncology, Rochester General Hospital, Rochester, New York, USA.

出版信息

JACC Case Rep. 2024 Aug 21;29(16):102461. doi: 10.1016/j.jaccas.2024.102461.

DOI:10.1016/j.jaccas.2024.102461
PMID:39295803
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11405962/
Abstract

Hypereosinophilic syndrome comprises a diverse and intricate array of rare disorders, exhibiting clinical manifestations that extend across various medical subspecialties. Within its myeloid form, chronic eosinophilic leukemia represents a rare myeloid malignancy characterized by severe hematological complications and distinctive organ dysfunction, notably affecting the cardiovascular system. This report presents a rare case of chronic eosinophilic leukemia and Loeffler syndrome with an initial presentation of ventricular tachycardia.

摘要

高嗜酸性粒细胞综合征包含一系列多样且复杂的罕见疾病,其临床表现涉及多个医学亚专业领域。在其髓系形式中,慢性嗜酸性粒细胞白血病是一种罕见的髓系恶性肿瘤,其特征为严重的血液学并发症和独特的器官功能障碍,尤其会影响心血管系统。本报告呈现了一例以室性心动过速为首发表现的慢性嗜酸性粒细胞白血病合并吕弗勒综合征的罕见病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b302/11405962/01eff172e028/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b302/11405962/31a6ad1bf1df/ga1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b302/11405962/ee3677ca572e/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b302/11405962/01eff172e028/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b302/11405962/31a6ad1bf1df/ga1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b302/11405962/ee3677ca572e/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b302/11405962/01eff172e028/gr2.jpg

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1
Incessant Ventricular Tachycardia: An Atypical Presentation of Chronic Eosinophilic Leukemia.持续性室性心动过速:慢性嗜酸性粒细胞白血病的一种非典型表现。
JACC Case Rep. 2024 Aug 21;29(16):102461. doi: 10.1016/j.jaccas.2024.102461.
2
Loeffler Endocarditis吕弗勒心内膜炎
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Hypereosinophilia and Left Ventricular Thrombus: A Case Report and Literature Review.嗜酸性粒细胞增多症与左心室血栓:一例报告及文献综述
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Bone marrow morphology is a strong discriminator between chronic eosinophilic leukemia, not otherwise specified and reactive idiopathic hypereosinophilic syndrome.骨髓形态学是慢性嗜酸性白血病、未分类和反应性特发性嗜酸性粒细胞增多综合征之间的有力鉴别诊断依据。
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Usefulness of three-dimensional echocardiography in the assessment of valvular involvement in Loeffler endocarditis.三维超声心动图在评估Löffler心内膜炎瓣膜受累情况中的应用价值
Echocardiography. 2017 Jul;34(7):1050-1056. doi: 10.1111/echo.13575. Epub 2017 Jun 9.

本文引用的文献

1
Approach to the patient with suspected hypereosinophilic syndrome.疑似嗜酸性粒细胞增多综合征患者的处理方法。
Hematology Am Soc Hematol Educ Program. 2022 Dec 9;2022(1):47-54. doi: 10.1182/hematology.2022000367.
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Diagnosis and treatment of eosinophilic myocarditis.嗜酸性粒细胞性心肌炎的诊断与治疗
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Fulminant Eosinophilic Myocarditis and VT Storm.暴发性嗜酸性粒细胞性心肌炎与室性心动过速风暴
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8
KIT D816V-associated systemic mastocytosis with eosinophilia and FIP1L1/PDGFRA-associated chronic eosinophilic leukemia are distinct entities.伴有嗜酸性粒细胞增多的KIT D816V相关系统性肥大细胞增多症和FIP1L1/PDGFRA相关慢性嗜酸性粒细胞白血病是不同的疾病实体。
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Ventricular remodeling in Loeffler endocarditis: implications for therapeutic decision making.勒夫勒心内膜炎中的心室重构:对治疗决策的影响
Eur J Heart Fail. 2005 Oct;7(6):1023-6. doi: 10.1016/j.ejheart.2005.06.004. Epub 2005 Sep 26.
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CHIC2 deletion, a surrogate for FIP1L1-PDGFRA fusion, occurs in systemic mastocytosis associated with eosinophilia and predicts response to imatinib mesylate therapy.CHIC2缺失作为FIP1L1-PDGFRA融合的替代指标,见于伴有嗜酸性粒细胞增多的系统性肥大细胞增多症,并可预测对甲磺酸伊马替尼治疗的反应。
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