Department of Obstetrics and Gynecology, Gyeongsang National University School of Medicine, Gyeongsang National University Hospital, Jinju 52727, Republic of Korea.
Institute of Medical Science, Gyeongsang National University, Jinju 52727, Republic of Korea.
Medicina (Kaunas). 2024 Oct 8;60(10):1645. doi: 10.3390/medicina60101645.
Angiomyofibroblastoma (AMFB) is an exceedingly rare mesenchymal tumor of the lower genital tract. AMFB primarily affects the pelviperineal region, especially the vulvar in premenopausal women. Typically, AMFB is a benign disease and does not have the potential for metastasis or recurrence, requiring complete surgical excision. Its accurate differentiation from aggressive angiomyxoma is critical due to varying prognoses. A 51-year-old woman, diagnosed with mucinous carcinoma of the breast, presented with a 12 cm abdominopelvic mass identified during breast cancer staging. Imaging suggested an ovarian origin; however, surgical exploration revealed a stalk-attached cystic mass in the anterior body of the uterus. Histopathology confirmed AMFB. Immunohistochemical analysis showed positivity for estrogen and progesterone receptors and smooth muscle actin. The patient continued breast cancer treatment postoperatively without pelvic mass recurrence or complications for a postoperative follow-up period of one year. This case highlights AMFB's potential uterine body origin, expending known tumor sites and complicating diagnosis due to overlapping features with other mesenchymal tumors. Accurate diagnosis using immunohistochemical markers and pathological features is essential to avoid unnecessary aggressive treatments. The uterine location in this case suggests a possible shared pathogenesis with uterine myomas, warranting further research into their connection. Reporting the first case of AMFB originating in the uterine body enhances understanding of this rare condition and underscores the importance of clinical awareness and precise diagnostic strategies to guide management and improve outcomes.
血管肌纤维母细胞瘤(AMFB)是一种极其罕见的女性生殖道间叶性肿瘤。AMFB 主要影响骨盆会阴区域,尤其是绝经前女性的外阴。通常情况下,AMFB 是一种良性疾病,不具有转移或复发的潜力,需要完全手术切除。由于预后不同,准确地区分其与侵袭性血管黏液瘤至关重要。一名 51 岁女性,诊断为乳腺黏液癌,在乳腺癌分期时发现 12cm 大小的腹盆腔肿块。影像学提示卵巢来源;然而,手术探查显示子宫前体附着于蒂的囊性肿块。组织病理学证实为 AMFB。免疫组化分析显示雌激素和孕激素受体以及平滑肌肌动蛋白阳性。该患者术后继续进行乳腺癌治疗,术后 1 年随访期间未出现盆腔肿块复发或并发症。该病例强调了 AMFB 可能的子宫体起源,扩展了已知的肿瘤部位,并由于与其他间叶性肿瘤具有重叠特征而使诊断复杂化。使用免疫组化标志物和病理特征进行准确诊断对于避免不必要的侵袭性治疗至关重要。该病例位于子宫体,提示与子宫肌瘤可能具有共同的发病机制,需要进一步研究其关联。首例 AMFB 起源于子宫体的报道增加了对这种罕见疾病的认识,并强调了临床意识和精确诊断策略的重要性,以指导管理并改善结局。