Lemos Leonor, Guimarães Henrique, Tavares Eduardo, Cardoso Tiago Miguel, Costa António, Poiarez Cristina
Anesthesiology and Critical Care, Centro Hospitalar Universitário de Santo António, Porto, PRT.
Cureus. 2024 Nov 1;16(11):e72824. doi: 10.7759/cureus.72824. eCollection 2024 Nov.
Cystic fibrosis (CF) is a genetic disorder that primarily affects the respiratory and gastrointestinal systems, often leading to significant perioperative challenges due to compromised lung function, recurrent infections, and chronic respiratory failure. Managing anesthesia in patients with CF requires careful consideration, particularly because of the increased risk of respiratory complications with general anesthesia (GA). Neuraxial anesthesia, such as spinal anesthesia, presents an alternative that can reduce the likelihood of postoperative pulmonary issues, including respiratory depression, hypoxemia, and atelectasis. However, spinal anesthesia is not without risk, particularly in the presence of coagulation abnormalities, which must be considered. We present the case of a 26-year-old male with severe CF, complicated by chronic respiratory failure and recurrent infections, who presented with acute appendicitis. The patient, with a history of bronchiectasis and chronic colonization by multidrug-resistant organisms, had stable but significantly impaired respiratory function, with a forced expiratory volume in one second (FEV1) of 1.62 L (38% predicted). He had a history of multiple hospital admissions for exacerbations of lung disease, none of which required mechanical ventilation or intensive care, with the most recent admission occurring 13 months prior to this event. Preoperative coagulation studies revealed an elevated international normalized ratio (INR) of 1.52 (normal range 0.8-1.2) and an activated partial thromboplastin time (APTT) of 38.1 seconds (normal <29.4 seconds), for which the patient received vitamin K without improvement. Despite these abnormalities, a thorough preoperative assessment and multidisciplinary discussion led to the decision to proceed with spinal anesthesia, carefully weighing the risks and benefits. An initial spinal anesthetic attempt with 2.0 mL of hyperbaric bupivacaine 0.5% (10 mg) and 2.5 mcg of sufentanil was administered at the L3-L4 interspace using a 27G Whitacre needle. Despite confirmed cerebrospinal fluid flow before injection, no sensory or motor block occurred, requiring an additional spinal injection. A second dose of 2.0 mL of hyperbaric bupivacaine 0.5% was administered at the L2-L3 interspace without sufentanil. A satisfactory sensory block to the T6 level was eventually obtained, allowing the appendectomy to proceed without intraoperative complications. Postoperatively, the patient was closely monitored in a high-dependency unit. He maintained stable respiratory function and experienced a smooth recovery, with minimal opioid use to avoid respiratory depression. The patient was discharged on the fifth postoperative day without respiratory or other anesthesia-related complications. This case highlights the importance of individualized care in CF patients undergoing surgery. Neuraxial anesthesia, when carefully planned and executed, can offer a safer alternative to GA by minimizing respiratory risks. However, the presence of coagulation abnormalities requires a detailed risk-benefit analysis, multidisciplinary collaboration, and vigilant intraoperative and postoperative care to ensure patient safety and optimize outcomes.
囊性纤维化(CF)是一种遗传性疾病,主要影响呼吸系统和胃肠道系统,由于肺功能受损、反复感染和慢性呼吸衰竭,常常导致重大的围手术期挑战。对CF患者进行麻醉管理需要仔细考虑,特别是因为全身麻醉(GA)会增加呼吸并发症的风险。神经轴索麻醉,如脊髓麻醉,是一种可以降低术后肺部问题可能性的替代方法,这些问题包括呼吸抑制、低氧血症和肺不张。然而,脊髓麻醉并非没有风险,特别是在存在凝血异常的情况下,必须加以考虑。我们报告一例26岁男性严重CF患者,并发慢性呼吸衰竭和反复感染,因急性阑尾炎就诊。该患者有支气管扩张病史,长期被多重耐药菌定植,呼吸功能稳定但严重受损,一秒用力呼气量(FEV1)为1.62 L(预测值的38%)。他有多次因肺部疾病加重入院的病史,均未需要机械通气或重症监护,最近一次入院发生在此次事件前13个月。术前凝血检查显示国际标准化比值(INR)升高至1.52(正常范围0.8 - 1.2),活化部分凝血活酶时间(APTT)为38.1秒(正常<29.4秒),患者接受维生素K治疗后无改善。尽管存在这些异常,但经过全面的术前评估和多学科讨论后,决定进行脊髓麻醉,仔细权衡风险和益处。在L3 - L4间隙使用27G Whitacre针给予初始脊髓麻醉,药物为2.0 mL 0.5%的重比重布比卡因(10 mg)和2.5 mcg舒芬太尼。尽管注射前确认有脑脊液流动,但未出现感觉或运动阻滞,需要再次进行脊髓注射。在L2 - L3间隙再次给予2.0 mL 0.5%的重比重布比卡因,未加舒芬太尼。最终获得了满意的T6水平感觉阻滞,阑尾切除术得以顺利进行,术中无并发症。术后,患者在高依赖病房接受密切监测。他的呼吸功能保持稳定,恢复顺利,使用最少的阿片类药物以避免呼吸抑制。患者术后第五天出院,无呼吸或其他与麻醉相关的并发症。该病例突出了对接受手术的CF患者进行个体化护理的重要性。精心规划和实施的神经轴索麻醉,通过将呼吸风险降至最低,可以为GA提供更安全的替代方案。然而,存在凝血异常需要进行详细的风险效益分析、多学科协作以及术中术后的密切监护,以确保患者安全并优化治疗结果。