Prasetyo Arif Tri
Division of Plastic Reconstructive and Aesthetic Surgery, Department of Surgery, Faculty of Medicine, Universitas Padjadjaran, Bandung, Indonesia.
Department of Plastic Reconstructive and Aesthetic Surgery, Universitas Padjadjaran Hospital, Sumedang, Indonesia.
Maxillofac Plast Reconstr Surg. 2025 Mar 17;47(1):7. doi: 10.1186/s40902-025-00461-0.
Craniofacial anomalies, particularly Tessier facial clefts, present significant surgical and functional challenges. Bilateral Tessier 3 and Tessier 0 clefts are extremely rare, often requiring complex reconstructive strategies. These clefts result in severe nasal deformities, including absent nasal septum, hypertelorism, and malpositioned alae nasi, affecting both appearance and function. Due to the lack of standardized approaches in such cases, this report highlights a staged surgical reconstruction aimed at restoring nasal structure and improving facial harmony, with a 12-month follow-up showing stable nasal contour and functional airway restoration.
A 16-year-old female presented with bilateral Tessier 3 and Tessier 0 clefts, exhibiting hypertelorism, a wide nasal dorsum, cranial displacement of the alae nasi, and an absent nasal septum. The patient underwent staged reconstruction. The first stage repositioned the alae nasi and created a functional nasal airway. In the second stage, costal cartilage was used to construct an L-shaped septal extension graft and dorsal onlay graft to restore nasal contour and stability. A subsequent procedure refined the nasal dorsum and approximated the alae nasi. Although orbital box osteotomy was planned to correct hypertelorism, the patient declined further intervention.
This case highlights the effectiveness of a staged reconstructive approach in addressing rare craniofacial anomalies. Twelve-month postoperative follow-up confirmed the stability of nasal contour, functional airway patency, and satisfactory facial symmetry. The decision to forgo orbital box osteotomy emphasizes the role of patient-centered care in craniofacial surgery. This case provides valuable insights for optimizing reconstructive techniques in complex facial clefts.
颅面畸形,尤其是特西尔面部裂隙,带来了重大的手术和功能挑战。双侧特西尔3型和特西尔0型裂隙极为罕见,通常需要复杂的重建策略。这些裂隙会导致严重的鼻畸形,包括鼻中隔缺失、两眼间距过宽以及鼻翼位置异常,影响外观和功能。由于此类病例缺乏标准化方法,本报告重点介绍了一种分阶段手术重建方法,旨在恢复鼻结构并改善面部协调性,12个月的随访显示鼻轮廓稳定且气道功能得以恢复。
一名16岁女性患有双侧特西尔3型和特西尔0型裂隙,表现为两眼间距过宽、鼻背宽阔、鼻翼向颅侧移位以及鼻中隔缺失。患者接受了分阶段重建手术。第一阶段重新定位鼻翼并建立功能性鼻气道。第二阶段,使用肋软骨构建L形鼻中隔延伸移植片和鼻背覆盖移植片,以恢复鼻轮廓和稳定性。随后的手术对鼻背进行了修整并使鼻翼更接近正常位置。尽管计划进行眶周截骨术以矫正两眼间距过宽,但患者拒绝进一步干预。
本病例突出了分阶段重建方法在处理罕见颅面畸形方面的有效性。术后12个月的随访证实了鼻轮廓的稳定性、气道功能通畅以及面部对称性令人满意。放弃眶周截骨术的决定强调了以患者为中心的护理在颅面外科手术中的作用。该病例为优化复杂面部裂隙的重建技术提供了宝贵的见解。