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Cystic fibrosis: a model for research and management of respiratory diseases.

作者信息

Felipe Montiel Almudena, Álvarez Fernández Antonio, Agustí Alvar, Polverino Eva

机构信息

Department of Respiratory Medicine (Adult Cystic Fibrosis Unit), Vall d'Hebron University Hospital, Vall d'Hebron Research Institute (VHIR). Universitat Autònoma de Barcelona (UAB), Barcelona, Spain.

Department of Respiratory Medicine (Adult Cystic Fibrosis Unit), Vall d'Hebron University Hospital, Vall d'Hebron Research Institute (VHIR), Universitat Autònoma de Barcelona (UAB), Barcelona, Spain.

出版信息

Ther Adv Respir Dis. 2025 Jan-Dec;19:17534666251329792. doi: 10.1177/17534666251329792. Epub 2025 Apr 1.

DOI:10.1177/17534666251329792
PMID:40170358
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11963717/
Abstract
摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5fc3/11963717/0fdc6e25aab5/10.1177_17534666251329792-fig1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5fc3/11963717/0fdc6e25aab5/10.1177_17534666251329792-fig1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/5fc3/11963717/0fdc6e25aab5/10.1177_17534666251329792-fig1.jpg

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本文引用的文献

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The In-between: Time to Talk About Bronchiectasis in Adolescents and Their Transition to Adult Care.中间地带：是时候谈谈青少年支气管扩张症及其向成人护理的过渡了。
Arch Bronconeumol. 2025 Apr;61(4):220-225. doi: 10.1016/j.arbres.2024.09.001. Epub 2024 Sep 24.
2
Cystic Fibrosis.囊性纤维化
N Engl J Med. 2023 Nov 2;389(18):1693-1707. doi: 10.1056/NEJMra2216474.
3
Theratyping cystic fibrosis patients to guide elexacaftor/tezacaftor/ivacaftor out-of-label prescription.对囊性纤维化患者进行基因分型，以指导依列卡福/替扎卡福/艾伐卡福的超说明书处方。
Eur Respir J. 2023 Oct 19;62(4). doi: 10.1183/13993003.00110-2023. Print 2023 Oct.
4
Design and implementation of a digital health home spirometry intervention for remote monitoring of lung transplant function.数字健康家庭肺量计干预设计与实现，用于远程监测肺移植功能。
J Heart Lung Transplant. 2023 Jun;42(6):828-837. doi: 10.1016/j.healun.2023.01.010. Epub 2023 Feb 2.
5
Cystic fibrosis transmembrane conductance regulator in COPD: a role in respiratory epithelium and beyond.慢性阻塞性肺疾病中的囊性纤维化跨膜电导调节因子：呼吸上皮细胞内外的作用。
Eur Respir J. 2023 Apr 1;61(4). doi: 10.1183/13993003.01307-2022. Print 2023 Apr.
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A review of the challenges, learnings and future directions of home handheld spirometry in interstitial lung disease.综述：间质性肺疾病家庭手持式肺功能测定的挑战、经验教训和未来方向。
Respir Res. 2022 Nov 11;23(1):307. doi: 10.1186/s12931-022-02221-4.
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