Pichi Francesco, Rissotto Federico, Qadha Khalid N, Smith Scott D, Khan Arif O
Eye Institute, Cleveland Clinic Abu Dhabi, Abu Dhabi, United Arab Emirates.
Cleveland Clinic Lerner College of Medicine, Case Western Reserve University, Cleveland, OH, USA.
Case Rep Ophthalmol. 2025 Mar 25;16(1):261-266. doi: 10.1159/000542415. eCollection 2025 Jan-Dec.
Vasoproliferative tumors (VPTs) can be associated with retinal dystrophy, but there are few well-documented cases and even fewer linked to Usher syndrome. Most reported cases are unilateral. The purpose of this report was to describe a case of bilateral sequential VPT in the context of -related Usher syndrome.
A 13-year-old female presented with pain in her left eye and no light perception in that eye. She was found to have left eye advanced neovascular glaucoma related to VPT in the context of -related Usher syndrome. Intraocular pressure and pain were controlled with external diode cyclodestruction. Almost 3 years later, early asymptomatic VPT was noted in the right eye during follow-up and was treated with laser photocoagulation.
Although VPT is typically unilateral, affected patients need careful follow-up for possible bilateral sequential disease. Early treatment avoids blinding complications.
血管增生性肿瘤（VPT）可与视网膜营养不良相关，但记录在案的病例很少，与Usher综合征相关的病例更少。大多数报告的病例为单侧。本报告的目的是描述一例与Usher综合征相关的双侧相继发生的VPT病例。
一名13岁女性因左眼疼痛且该眼无光感就诊。她被发现患有与Usher综合征相关的、由VPT引起的左眼晚期新生血管性青光眼。通过外部二极管睫状体破坏术控制了眼压和疼痛。近3年后，随访期间右眼发现早期无症状VPT，并接受了激光光凝治疗。
虽然VPT通常为单侧，但患病患者需要仔细随访，以排查可能出现的双侧相继发病情况。早期治疗可避免致盲并发症。
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