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一例罕见的分泌儿茶酚胺的肾上腺髓脂肪瘤

A Rare Case of Catecholamine-Secreting Adrenal Myelolipoma.

作者信息

Jain Veenu, Aggarwal Anshita, Kulshreshtha Bindu, Singh Preeti, Goel Hemant

机构信息

Department of Endocrinology, Atal Bihari Vajpayee Institute of Medical Sciences and Dr. Ram Manohar Lohia Hospital, New Delhi, India.

Department of Pathology, Atal Bihari Vajpayee Institute of Medical Sciences and Dr. Ram Manohar Lohia Hospital, New Delhi, India.

出版信息

J ASEAN Fed Endocr Soc. 2025 May;40(1):104-107. doi: 10.15605/jafes.040.01.15. Epub 2025 Apr 25.

DOI:10.15605/jafes.040.01.15
PMID:40416490
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12097973/
Abstract

Adrenal myelolipoma (AML) is a rare, benign, asymptomatic, nonfunctioning tumor of the adrenal cortex detected incidentally. AML can be accompanied by several other endocrine disorders simultaneously. Here, we report a case of a 36-year-old female with primary hypothyroidism and metabolic syndrome accompanied by severe hypertension and pheochromocytoma. However, the histopathological examination of the excised adrenal gland confirmed myelolipoma. Following surgery, her plasma nor-metanephrine levels decreased to normal values and the patient became normotensive, which suggested that the mass was functioning.

摘要

肾上腺髓质脂肪瘤(AML)是一种罕见的、良性的、无症状的、无功能的肾上腺皮质肿瘤,多为偶然发现。AML可同时伴有其他几种内分泌疾病。在此,我们报告一例36岁女性,患有原发性甲状腺功能减退症和代谢综合征,并伴有严重高血压和嗜铬细胞瘤。然而,切除的肾上腺组织病理学检查证实为髓质脂肪瘤。手术后,她的血浆去甲变肾上腺素水平降至正常,血压也恢复正常,这表明该肿块具有功能。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bb23/12097973/8c2999f6d799/JAFES-40-1-104-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bb23/12097973/b3d1d6d70cc6/JAFES-40-1-104-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bb23/12097973/f3d0cae7909f/JAFES-40-1-104-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bb23/12097973/b48bcee2c5a7/JAFES-40-1-104-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bb23/12097973/8c2999f6d799/JAFES-40-1-104-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bb23/12097973/b3d1d6d70cc6/JAFES-40-1-104-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bb23/12097973/f3d0cae7909f/JAFES-40-1-104-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bb23/12097973/b48bcee2c5a7/JAFES-40-1-104-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/bb23/12097973/8c2999f6d799/JAFES-40-1-104-g004.jpg

相似文献

1
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本文引用的文献

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The clinical conundrum of a catecholamine secreting giant adrenal myelolipoma.分泌儿茶酚胺的巨大肾上腺髓质脂肪瘤的临床难题。
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Endocrine. 2018 Jan;59(1):7-15. doi: 10.1007/s12020-017-1473-4. Epub 2017 Nov 21.
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Hypothyroidism in India: more to be done.印度的甲状腺功能减退症:仍有许多工作要做。
Lancet Diabetes Endocrinol. 2014 Oct;2(10):778. doi: 10.1016/S2213-8587(14)70208-6.
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Thyroid function and obesity.甲状腺功能与肥胖
J Clin Res Pediatr Endocrinol. 2013;5 Suppl 1(Suppl 1):40-4. doi: 10.4274/jcrpe.856. Epub 2012 Nov 1.
10
Left-sided giant adrenal myelolipoma secreting catecholamine.分泌儿茶酚胺的左侧巨大肾上腺髓质脂肪瘤。
Indian J Pathol Microbiol. 2012 Jul-Sep;55(3):389-91. doi: 10.4103/0377-4929.101755.