Road J D, Jacques J, Sparling J R
Am Rev Respir Dis. 1985 Dec;132(6):1368-70. doi: 10.1164/arrd.1985.132.6.1368.
An unusual case of recurrent hemoptysis in a 56-yr-old woman is presented. After all the usual investigations for hemoptysis, left lower lobectomy revealed medial dissection of small and medium-sized pulmonary arteries with evidence of amyloid deposition. The patient subsequently developed the clinical picture of diffuse alveolar septal amyloidosis in association with primary amyloidosis. Pulmonary artery dissection is briefly reviewed, and vascular amyloidosis is presented as the probable origin in this case.
本文报道了一例56岁女性复发性咯血的罕见病例。在对咯血进行了所有常规检查后,左肺下叶切除术显示中小肺动脉内侧剥离,并伴有淀粉样蛋白沉积的证据。该患者随后出现了与原发性淀粉样变性相关的弥漫性肺泡间隔淀粉样变性的临床表现。本文简要回顾了肺动脉剥离,并提出血管淀粉样变性可能是该病例的病因。