Arya S, Hong R, Gilbert E F
Pediatr Pathol. 1985;3(2-4):129-41. doi: 10.3109/15513818509078779.
Two cases of reactive hemophagocytic syndrome (RHS) are reported, and the clinical and pathological features are compared with other histiocytic proliferative disorders, including familial hemophagocytic lymphohistiocytosis (FHL) and malignant histiocytosis. RHS can be associated with a variety of infections, including viral, bacterial, fungal, and parasitic. RHS may also be familial as exemplified by our 2 cases in siblings. The isolation of an effective agent appears to be the only criterion by which a diagnosis of RHS can be made.
报告了2例反应性噬血细胞综合征（RHS），并将其临床和病理特征与其他组织细胞增生性疾病进行比较，包括家族性噬血细胞性淋巴组织细胞增生症（FHL）和恶性组织细胞增多症。RHS可与多种感染相关，包括病毒、细菌、真菌和寄生虫感染。RHS也可能具有家族性，如我们报告的2例同胞病例所示。分离出有效病原体似乎是诊断RHS的唯一标准。
