Malakooti Mohammad, Heidari Afshin, Motieian Mahsa, Farid Armita, Neshat Sina, Bidares Matin, Jahanshahi Fatemeh, Gorgani Milad, Shayestehyekta Hossein, Moradi Hazhir, Valipoor Aydin
Department of Neurology, Faculty of Medicine, Iran University of Medical Sciences, Tehran, Iran.
School of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran.
Tremor Other Hyperkinet Mov (N Y). 2025 Sep 24;15:45. doi: 10.5334/tohm.1074. eCollection 2025.
This review aims to provide a comprehensive understanding of Lance-Adams Syndrome (LAS), focusing on its pathophysiology, diagnosis, management, and patient outcomes.
Utilizing the PICO framework, articles describing known cases of LAS and interventions were included, with no specific comparisons. The search was conducted in Google Scholar, PubMed, and Scopus databases.
LAS is characterized by action myoclonus and related symptoms. Imbalances in neurotransmitters and involvement of brain areas like the cerebellum, thalamus, and basal ganglia play a role in its pathophysiology. Diagnosis primarily relies on symptom history post-anoxic events, and treatments vary in effectiveness. LAS generally carries a more favorable functional prognosis than early post-anoxic status myoclonus, but often remains chronic and disabling.
LAS is a complex and rare neurological condition requiring early diagnosis and specific interventions. The compiled information provides a comprehensive overview, assisting clinicians in understanding and managing LAS. This review emphasizes the need for ongoing research and individualized patient care strategies, seeking to enhance overall patient quality of life.
本综述旨在全面了解兰斯-亚当斯综合征(LAS),重点关注其病理生理学、诊断、管理及患者预后。
采用PICO框架,纳入描述LAS已知病例及干预措施的文章,不进行特定比较。检索在谷歌学术、PubMed和Scopus数据库中进行。
LAS的特征为动作性肌阵挛及相关症状。神经递质失衡以及小脑、丘脑和基底神经节等脑区的参与在其病理生理学中起作用。诊断主要依赖于缺氧事件后的症状史,治疗效果各异。与早期缺氧后状态性肌阵挛相比,LAS通常具有更有利的功能预后,但往往仍为慢性且致残。
LAS是一种复杂且罕见的神经系统疾病,需要早期诊断和特定干预。汇总的信息提供了全面概述,有助于临床医生理解和管理LAS。本综述强调了持续研究和个体化患者护理策略的必要性,旨在提高患者的整体生活质量。