Shuangshoti S, Chongchet V
J Neurol Neurosurg Psychiatry. 1979 Jun;42(6):524-8. doi: 10.1136/jnnp.42.6.524.
Malignant mesenchymoma within the right ulnar nerve of an 8 year old boy is described. The patient did not have stigmata of von Recklinghausen's neurofibromatosis. The growing and painful tumour was excised five and a half detection, and recurred five months later. Mingling of the nerve sheath sarcoma and rhabdomyosarcoma was noted within the same mass which was separated from the adjacent striated muscles. It is suggested that this mesenchymoma arose from mesenchymal cells or cells of mesenchymal type comprising the peripheral nerve sheath which is derived from ectomesenchyme of the neural crest.
本文描述了一名8岁男孩右侧尺神经内的恶性间叶瘤。该患者没有冯·雷克林豪森神经纤维瘤病的体征。生长且疼痛的肿瘤在发现五个半月后被切除,五个月后复发。在与相邻横纹肌分离的同一肿块内,观察到神经鞘肉瘤和平滑肌肉瘤的混合。提示这种间叶瘤起源于构成周围神经鞘的间充质细胞或间充质类型的细胞,而周围神经鞘源自神经嵴的外胚层间充质。