Prud'homme G J, Balderas R S, Dixon F J, Theofilopoulos A N
J Exp Med. 1983 Jun 1;157(6):1815-27. doi: 10.1084/jem.157.6.1815.
B cell hyperactivity, a feature common to all lupus-prone murine strains, may be caused by hyperresponsiveness to, overproduction of, or bypassing of certain signals required for B cell activation, proliferation, and differentiation. In this study, we have compared the responses of B cells from three lupus-prone strains of mice (BXSB males, MRL and NZB/W females) and normal strains in a number of assays for which two or more signals are required to obtain a response. In medium to low density cultures of B cells from BXSB and NZB/W but not MRL/l lupus mice, the cells' proliferation induced by bacterial lipopolysaccharide (LPS) or anti-mu antibody was much higher than that of B cells from normal controls. At low B cell density, polyclonal activation by these substances and subsequent Ig secretion were dependent on accessory signals present in supernatants of concanavalin A-treated normal lymphocytes (CAS) or on the MRL/l proliferating T cell-derived B cell differentiation factor (L-BCDF) in both lupus-prone and immunologically normal mice. However, the responses of B cells from BXSB and NZB/W, but not MRL/l, mice to these accessory signals were higher than those of normal mice. Ig synthesis by fresh B cells of BXSB and NZB/W mice cultured in the absence of mitogens but in the presence of CAS or L-BCDF was higher than by similar cells from other strains, suggesting an increased frequency of B cells activated in vivo in these two autoimmune strains of mice. The patterns of IgG subclass secretion in response to LPS (without added CAS or L-BCDF) were abnormal in all lupus strains, with a predominance of IgG2b and/or IgG2a and low levels of IgG3, contrary to normal B cells for which IgG3 synthesis predominated. However, IgG1 synthesis in vitro by autoimmune and normal B cells alike was highly dependent on T cell-derived soluble mediators. Antigen-specific responses to SRBC in vitro of B cells from all lupus strains, like those of B cells from normal strains, required a minimum of three signals (antigen, LPS, T cell-derived antigen nonspecific helper factors). Yet, once triggered, B cells of BXSB and NZB/W mice gave higher responses than those of the other strains. We conclude that B cells of lupus mice have signal requirements similar to those of normal mice. Nevertheless, B cells of BXSB and NZB/W, but not MRL/l, lupus mice hyperrespond or process some accessory signals abnormally.
B细胞功能亢进是所有易患狼疮的小鼠品系共有的特征,可能是由于对B细胞激活、增殖和分化所需的某些信号反应过度、产生过多或绕过这些信号所致。在本研究中,我们比较了三种易患狼疮的小鼠品系(BXSB雄性、MRL和NZB/W雌性)以及正常品系的B细胞在一些需要两种或更多信号才能产生反应的试验中的反应。在来自BXSB和NZB/W但不是MRL/l狼疮小鼠的B细胞的中低密度培养中,细菌脂多糖(LPS)或抗μ抗体诱导的细胞增殖远高于正常对照的B细胞。在低B细胞密度下,这些物质的多克隆激活及随后的Ig分泌依赖于伴刀豆球蛋白A处理的正常淋巴细胞(CAS)上清液中存在的辅助信号,或依赖于易患狼疮和免疫正常小鼠中MRL/l增殖性T细胞衍生的B细胞分化因子(L-BCDF)。然而,来自BXSB和NZB/W但不是MRL/l小鼠的B细胞对这些辅助信号的反应高于正常小鼠。在无丝裂原但有CAS或L-BCDF存在的情况下培养的BXSB和NZB/W小鼠新鲜B细胞的Ig合成高于其他品系的类似细胞,这表明在这两种自身免疫性小鼠品系中,体内被激活的B细胞频率增加。在所有狼疮品系中,对LPS(不添加CAS或L-BCDF)的IgG亚类分泌模式均异常,以IgG2b和/或IgG2a为主,IgG3水平较低,这与以IgG3合成为主的正常B细胞相反。然而,自身免疫性和正常B细胞在体外的IgG1合成高度依赖于T细胞衍生的可溶性介质。所有狼疮品系的B细胞在体外对SRBC的抗原特异性反应,与正常品系的B细胞一样,至少需要三种信号(抗原、LPS、T细胞衍生的抗原非特异性辅助因子)。然而,一旦被触发,BXSB和NZB/W小鼠的B细胞反应比其他品系更高。我们得出结论,狼疮小鼠的B细胞与正常小鼠具有相似的信号需求。然而,BXSB和NZB/W而非MRL/l狼疮小鼠的B细胞反应过度或对某些辅助信号处理异常。