Bass N M, Burroughs A K, Scheuer P J, James D G, Sherlock S
Gut. 1982 May;23(5):417-21. doi: 10.1136/gut.23.5.417.
Two West Indian patients with Kveim-biopsy proven sarcoidosis developed chronic cholestatic liver disease, clinically and biochemically similar to primary biliary cirrhosis. Liver histology revealed multiple granulomas with reduction in bile ducts and, in one patient, progression to biliary cirrhosis. Portal hypertension was present in both patients leading to severe variceal haemorrhage in one. Mitochondrial antibody was negative in both patients and when used in conjunction with the Kveim-Siltzbach skin test serves to differentiate chronic intrahepatic cholestasis secondary to sarcoidosis from primary biliary cirrhosis.
两名经克维姆活检证实为结节病的西印度患者出现了慢性胆汁淤积性肝病,临床和生化表现与原发性胆汁性肝硬化相似。肝脏组织学检查发现多个肉芽肿,胆管减少,其中一名患者发展为胆汁性肝硬化。两名患者均存在门静脉高压,其中一名导致严重的静脉曲张出血。两名患者的线粒体抗体均为阴性,结合克维姆-西尔茨巴赫皮肤试验有助于将结节病继发的慢性肝内胆汁淤积与原发性胆汁性肝硬化区分开来。