• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

模仿腰椎管狭窄综合征的慢性炎症性脱髓鞘性多发性神经病。

Chronic inflammatory demyelinating polyneuropathy mimicking a lumbar spinal stenosis syndrome.

作者信息

Ginsberg L, Platts A D, Thomas P K

机构信息

Department of Clinical Neurosciences, Royal Free Hospital School of Medicine, London, UK.

出版信息

J Neurol Neurosurg Psychiatry. 1995 Aug;59(2):189-91. doi: 10.1136/jnnp.59.2.189.

DOI:10.1136/jnnp.59.2.189
PMID:7629539
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC486000/
Abstract

A patient with chronic inflammatory demyelinating polyneuropathy (CIDP) established by biopsy developed cauda equina symptoms due to swelling of the nerve roots in the lumbar spinal canal. Magnetic resonance imaging of the lumbar spine showed profoundly thickened nerve roots from the level of the conus medullaris, filling the caudal thecal sac. Immunosuppressant treatment produced partial clinical and radiological resolution. This case shows that spinal compressive syndromes may occur in acquired hypertrophic neuropathies as well as in hereditary motor and sensory neuropathy and expands the range of the clinical presentation of CIDP.

摘要

一名经活检确诊为慢性炎症性脱髓鞘性多发性神经病(CIDP)的患者,因腰椎管内神经根肿胀出现马尾综合征症状。腰椎磁共振成像显示,从脊髓圆锥水平开始神经根明显增粗,充满了尾侧硬膜囊。免疫抑制治疗使临床症状和影像学表现部分缓解。该病例表明,脊髓压迫综合征可能发生于获得性肥厚性神经病以及遗传性运动和感觉神经病,扩大了CIDP的临床表现范围。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3bf8/486000/ab958c246aa3/jnnpsyc00020-0080-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3bf8/486000/e34dda332e16/jnnpsyc00020-0080-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3bf8/486000/ab958c246aa3/jnnpsyc00020-0080-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3bf8/486000/e34dda332e16/jnnpsyc00020-0080-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3bf8/486000/ab958c246aa3/jnnpsyc00020-0080-b.jpg

相似文献

1
Chronic inflammatory demyelinating polyneuropathy mimicking a lumbar spinal stenosis syndrome.模仿腰椎管狭窄综合征的慢性炎症性脱髓鞘性多发性神经病。
J Neurol Neurosurg Psychiatry. 1995 Aug;59(2):189-91. doi: 10.1136/jnnp.59.2.189.
2
Magnetic resonance imaging of the cauda equina in chronic inflammatory demyelinating polyneuropathy.慢性炎症性脱髓鞘性多发性神经病马尾神经的磁共振成像
Ann Neurol. 1993 Mar;33(3):311-3. doi: 10.1002/ana.410330314.
3
Chronic inflammatory demyelinating polyneuropathy (CIDP) in diabetics.糖尿病患者的慢性炎症性脱髓鞘性多发性神经病(CIDP)
J Neurol Sci. 1996 Oct;142(1-2):59-64. doi: 10.1016/0022-510x(96)00126-8.
4
Nerve root hypertrophy as the cause of lumbar stenosis in chronic inflammatory demyelinating polyradiculoneuropathy.神经根肥大作为慢性炎症性脱髓鞘性多发性神经根神经病中腰椎管狭窄的病因
Muscle Nerve. 1996 Jul;19(7):892-6. doi: 10.1002/(SICI)1097-4598(199607)19:7<892::AID-MUS12>3.0.CO;2-L.
5
Chronic inflammatory demyelinating polyneuropathy in a child: clinical-spinal MR imaging correlation.儿童慢性炎症性脱髓鞘性多发性神经病:临床与脊髓磁共振成像的相关性
Singapore Med J. 2004 Nov;45(11):536-7.
6
Acquired inflammatory demyelinating polyneuropathies: clinical and electrodiagnostic features.获得性炎性脱髓鞘性多发性神经病:临床及电诊断特征
Muscle Nerve. 1989 Jun;12(6):435-51. doi: 10.1002/mus.880120602.
7
Chronic inflammatory demyelinating polyneuropathy in childhood: clinical and electrophysiological features.儿童慢性炎症性脱髓鞘性多发性神经病:临床及电生理特征
Childs Nerv Syst. 1991 Aug;7(4):191-6. doi: 10.1007/BF00249394.
8
Nerve root hypertrophy in chronic inflammatory demyelinating polyneuropathy.
Muscle Nerve. 1994 Feb;17(2):168-70. doi: 10.1002/mus.880170206.
9
Circulatory dynamics of the cauda equina in lumbar canal stenosis using dynamic contrast-enhanced magnetic resonance imaging.使用动态对比增强磁共振成像评估腰椎管狭窄症中马尾神经的循环动力学
Spine J. 2015 Oct 1;15(10):2132-41. doi: 10.1016/j.spinee.2015.05.014. Epub 2015 May 18.
10
Atypical electrophysiologic findings in chronic inflammatory demyelinating polyneuropathy (CIDP)--diagnosis confirmed by nerve biopsy.慢性炎症性脱髓鞘性多发性神经病(CIDP)的非典型电生理表现——神经活检确诊
Neurophysiol Clin. 2004 Apr;34(2):71-9. doi: 10.1016/j.neucli.2004.01.004.

引用本文的文献

1
Nerve Enlargement in Patients with INF2 Variants Causing Peripheral Neuropathy and Focal Segmental Glomerulosclerosis.携带导致周围神经病变和局灶节段性肾小球硬化的INF2变异体患者的神经肿大
Biomedicines. 2025 Jan 8;13(1):127. doi: 10.3390/biomedicines13010127.
2
Original Surgical Treatment and Long-term Follow-up for Chronic Inflammatory Demyelinating Polyradiculoneuropathy Causing a Compressive Cervical Myelopathy: Review of the Literature.慢性炎症性脱髓鞘性多发性神经根神经病导致压迫性颈髓病的原手术治疗及长期随访:文献综述
Neurospine. 2022 Jun;19(2):472-477. doi: 10.14245/ns.2143232.616. Epub 2022 May 17.
3
Length-dependent changes of lower limb muscle morphology in Chronic Inflammatory Demyelinating Polyneuropathy assessed with magnetic resonance imaging.

本文引用的文献

1
Observations on hypertrophic neuropathy of Dejerine and Sottas.关于德热里纳和索塔斯肥大性神经病的观察
Neurology. 1962 Oct;12:712-24. doi: 10.1212/wnl.12.10.712.
2
[Hypertrophic polyneuritis in adults (non-familial) with spasmodic paraparesis].[成人(非家族性)伴有痉挛性截瘫的肥厚性多神经炎]
Rev Neurol (Paris). 1952;86(6):695-8.
3
Magnetic resonance imaging of the cauda equina in chronic inflammatory demyelinating polyneuropathy.慢性炎症性脱髓鞘性多发性神经病马尾神经的磁共振成像
利用磁共振成像评估慢性炎症性脱髓鞘性多发性神经病下肢肌肉形态的长度依赖性变化。
Eur J Transl Myol. 2021 Nov 18;31(4):10200. doi: 10.4081/ejtm.2021.10200.
4
Pain in Chronic Inflammatory Demyelinating Polyradiculoneuropathy: A Systematic Review and Meta-Analysis.慢性炎症性脱髓鞘性多发性神经根神经病中的疼痛:一项系统评价和荟萃分析
Pain Ther. 2019 Dec;8(2):177-185. doi: 10.1007/s40122-019-0128-y. Epub 2019 Jun 14.
5
Could Spinal Canal Compression be a Cause of Polyneuropathy?椎管狭窄会是多发性神经病的一个病因吗?
Clin Pract. 2016 Apr 11;6(1):816. doi: 10.4081/cp.2016.816. eCollection 2016 Mar 25.
6
Underestimated associated features in CMT neuropathies: clinical indicators for the causative gene?遗传性运动感觉神经病(CMT)中被低估的相关特征:致病基因的临床指标?
Brain Behav. 2016 Mar 4;6(4):e00451. doi: 10.1002/brb3.451. eCollection 2016 Apr.
7
A case of cauda equina syndrome in early-onset chronic inflammatory demyelinating polyneuropathy clinically similar to charcot-marie-tooth disease type 1.一例早发型慢性炎症性脱髓鞘性多发性神经病合并马尾综合征,临床表现类似于1型遗传性运动感觉神经病。
J Korean Neurosurg Soc. 2014 Jun;55(6):370-4. doi: 10.3340/jkns.2014.55.6.370. Epub 2014 Jun 30.
8
Peripheral neuropathy: clinical and electrophysiological considerations.周围神经病:临床和电生理学考虑。
Neuroimaging Clin N Am. 2014 Feb;24(1):49-65. doi: 10.1016/j.nic.2013.03.023. Epub 2013 May 25.
9
[Hereditary motor and sensory neuropathy (HMSN) with hypertrophy of the cauda equina and concomitant demyelinating white matter lesions].伴有马尾肥大及伴随脱髓鞘性白质病变的遗传性运动和感觉神经病(HMSN)
Radiologe. 2005 Jul;45(7):593-6. doi: 10.1007/s00117-003-0967-7.
10
Marked hypertrophy of the cauda equina in a patient with chronic inflammatory demyelinating polyradiculoneuropathy presenting as lumbar stenosis.
J Neurol. 2005 Feb;252(2):239-40. doi: 10.1007/s00415-005-0632-3.
Ann Neurol. 1993 Mar;33(3):311-3. doi: 10.1002/ana.410330314.
4
Hypertrophic neuropathy with spinal cord compression.伴有脊髓受压的肥厚性神经病
Surg Neurol. 1982 Oct;18(4):237-40. doi: 10.1016/0090-3019(82)90330-5.
5
Myelographic findings in hypertrophic interstitial neuritis.肥厚性间质性神经炎的脊髓造影表现
Am J Roentgenol Radium Ther Nucl Med. 1965 Dec;95(4):947-8. doi: 10.2214/ajr.95.4.947.
6
Hypertrophic neuropathy. Plain film and myelographic changes.
Radiology. 1972 May;103(2):319-22. doi: 10.1148/103.2.319.
7
Radiological findings in a case of Charcot-Marie-Tooth disease.一例夏科-马里-图思病的放射学表现。
Br J Radiol. 1985 Oct;58(694):1017-20. doi: 10.1259/0007-1285-58-694-1017.
8
Nerve root enlargement in Charcot-Marie-Tooth disease: CT appearance.
Radiology. 1986 Dec;161(3):784. doi: 10.1148/radiology.161.3.3786733.
9
Compression syndromes due to hypertrophic nerve roots in hereditary motor sensory neuropathy type I.
Neurology. 1989 Sep;39(9):1173-7. doi: 10.1212/wnl.39.9.1173.
10
Myelographic evidence for nerve root enlargement in a case of Charcot-Marie-Tooth disease.
Neuroradiology. 1976 Jul 30;11(4):165-7. doi: 10.1007/BF00346073.