Pivetti-Pezzi P, Torce C, Colabelli-Gisoldi R A, Vitale A, Baccari A, Pacchiarotti A
Institute of Ophthalmology, University La Sapienza, Roma, Italy.
Eur J Ophthalmol. 1995 Jan-Mar;5(1):59-62. doi: 10.1177/112067219500500110.
Sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman disease) is a non-hereditary histiocytic proliferative disorder affecting young people, with extranodal manifestations in 28-43% of cases. Eye involvement is infrequent. Lymphoproliferation in the soft tissues of the orbit and in the lids has been reported in 12% of cases but intraocular involvement is rare. We describe the case of a 12-year-old boy affected by Rosai-Dorfman disease with bilateral relapsing uveitis and papilledema that appeared four years before the onset of lymphadenopathy.
伴巨大淋巴结病的窦性组织细胞增生症（罗萨伊-多夫曼病）是一种影响年轻人的非遗传性组织细胞增生性疾病，28%-43%的病例有结外表现。眼部受累情况不常见。据报道，12%的病例出现眼眶软组织和眼睑的淋巴细胞增生，但眼内受累罕见。我们描述了一名12岁男孩的病例，他患有罗萨伊-多夫曼病，在淋巴结病出现前四年就出现了双侧复发性葡萄膜炎和视乳头水肿。
