家族性噬血细胞性淋巴组织细胞增生症。两例报告及临床病理回顾。
Familial erythrophagocytic lymphohistocytosis. Report of two cases and clinicopathologic review.
作者信息
Perry M C, Harrison E G, Burgert E O, Gilchrist G S
出版信息
Cancer. 1976 Jul;38(1):209-18. doi: 10.1002/1097-0142(197607)38:1<209::aid-cncr2820380132>3.0.co;2-w.
Abstract
An unusual syndrome of hepatosplenomegaly and fever followed by rapid deterioration and death has been described in 38 children from 21 families. Pancytopenia, liver dysfunction, and bleeding developed prior to death from hemorrhage, sepsis, or lymphocytic meningitis. This report reviews the literature and adds a set of twins to the reported cases.
摘要
在来自21个家庭的38名儿童中，曾描述过一种不寻常的综合征，其表现为肝脾肿大和发热，随后迅速恶化并死亡。全血细胞减少、肝功能障碍和出血在因出血、败血症或淋巴细胞性脑膜炎死亡之前就已出现。本报告回顾了文献，并在报告病例中增加了一对双胞胎。
Zotero 插件