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Mitochondrial damage: an important feature in a number of inborn errors of metabolism?

作者信息

Heales S J, Bolaños J P, Brand M P, Clark J B, Land J M

机构信息

Department of Clinical Biochemistry, National Hospital for Neurology and Neurosurgery, London, UK.

出版信息

J Inherit Metab Dis. 1996;19(2):140-2. doi: 10.1007/BF01799414.

DOI:10.1007/BF01799414
PMID:8739950
Abstract
摘要

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Mitochondrial damage: an important feature in a number of inborn errors of metabolism?线粒体损伤：多种先天性代谢缺陷中的一个重要特征？
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本文引用的文献

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Depletion of brain glutathione is accompanied by impaired mitochondrial function and decreased N-acetyl aspartate concentration.
Neurochem Res. 1995 Jan;20(1):31-8. doi: 10.1007/BF00995149.
2
Effect of peroxynitrite on the mitochondrial respiratory chain: differential susceptibility of neurones and astrocytes in primary culture.过氧亚硝酸盐对线粒体呼吸链的影响：原代培养神经元和星形胶质细胞的不同易感性
J Neurochem. 1995 May;64(5):1965-72. doi: 10.1046/j.1471-4159.1995.64051965.x.
3
In search of a function for tetrahydrobiopterin in the biosynthesis of nitric oxide.寻找四氢生物蝶呤在一氧化氮生物合成中的作用。
癸酸治疗对复杂I型缺陷 Leigh 综合征患者成纤维细胞线粒体功能的多效性作用。
J Inherit Metab Dis. 2016 May;39(3):415-426. doi: 10.1007/s10545-016-9930-4. Epub 2016 Apr 14.
4
Drug-Induced Mitochondrial Toxicity.药物诱导的线粒体毒性
Drug Saf. 2016 Jul;39(7):661-74. doi: 10.1007/s40264-016-0417-x.
5
Zellweger syndrome and secondary mitochondrial myopathy.泽韦格综合征和继发性线粒体肌病。
Eur J Pediatr. 2015 Apr;174(4):557-63. doi: 10.1007/s00431-014-2431-2. Epub 2014 Oct 7.
6
Development of pharmacological strategies for mitochondrial disorders.线粒体疾病药理学策略的发展
Br J Pharmacol. 2014 Apr;171(8):1798-817. doi: 10.1111/bph.12456.
7
Oxidative stress in phenylketonuria: what is the evidence?苯丙酮尿症中的氧化应激：有何证据？
Cell Mol Neurobiol. 2011 Jul;31(5):653-62. doi: 10.1007/s10571-011-9693-2. Epub 2011 Apr 23.
8
Glutathione deficiency in patients with mitochondrial disease: implications for pathogenesis and treatment.线粒体疾病患者的谷胱甘肽缺乏：对发病机制和治疗的影响。
J Inherit Metab Dis. 2005;28(1):81-8. doi: 10.1007/s10545-005-4160-1.
9
The role of oxidative damage in the neuropathology of organic acidurias: insights from animal studies.氧化损伤在有机酸尿症神经病理学中的作用：来自动物研究的见解。
J Inherit Metab Dis. 2004;27(4):427-48. doi: 10.1023/B:BOLI.0000037353.13085.e2.
Naunyn Schmiedebergs Arch Pharmacol. 1995 May;351(5):453-63. doi: 10.1007/BF00171035.
4
The oxidative inactivation of mitochondrial electron transport chain components and ATPase.线粒体电子传递链组分和ATP酶的氧化失活。
J Biol Chem. 1990 Sep 25;265(27):16330-6.
5
Cytochrome c oxidase and cardiolipin alterations in response to skeletal muscle ischaemia and reperfusion.细胞色素c氧化酶和心磷脂对骨骼肌缺血再灌注的反应变化
Acta Physiol Scand. 1990 Feb;138(2):107-14. doi: 10.1111/j.1748-1716.1990.tb08822.x.
6
Glutathione deficiency leads to mitochondrial damage in brain.
Proc Natl Acad Sci U S A. 1991 Mar 1;88(5):1913-7. doi: 10.1073/pnas.88.5.1913.
7
Ca2+/calmodulin-dependent formation of hydrogen peroxide by brain nitric oxide synthase.脑一氧化氮合酶通过钙/钙调蛋白依赖性方式生成过氧化氢。
Biochem J. 1992 Feb 1;281 ( Pt 3)(Pt 3):627-30. doi: 10.1042/bj2810627.