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多发性肌炎和干燥综合征合并闭塞性细支气管炎并机化性肺炎。

Polymyositis and Sjögren's syndrome associated with bronchiolitis obliterans organizing pneumonia.

作者信息

Imasaki T, Yoshii A, Tanaka S, Ogura T, Ishikawa A, Takahashi T

机构信息

Department of Internal Medicine, Isehara Kyodo Hospital.

出版信息

Intern Med. 1996 Mar;35(3):231-5. doi: 10.2169/internalmedicine.35.231.

Abstract

Bronchiolitis obliterans organizing pneumonia (BOOP) occurred in a 53-year-old woman with well-documented Sjögren's syndrome (SjS) and polymyositis (PM). BOOP has often been reported as a pulmonary manifestation of collagen vascular diseases, mainly rheumatoid arthritis (RA), but the association of BOOP and PM has rarely been documented. A search of the literature showed only 16 case reports of BOOP associated with polymyositis-dermatomyositis (PM-DM). It is interesting that BOOP occurred prior to PM-DM, while it is commonly believed to occur after RA.

摘要

一名53岁患有明确记录的干燥综合征(SjS)和多发性肌炎(PM)的女性发生了闭塞性细支气管炎伴机化性肺炎(BOOP)。BOOP常被报道为胶原血管疾病的肺部表现,主要是类风湿关节炎(RA),但BOOP与PM的关联鲜有记录。文献检索仅显示16例与多发性肌炎-皮肌炎(PM-DM)相关的BOOP病例报告。有趣的是,BOOP发生在PM-DM之前,而通常认为它发生在RA之后。

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