完全性先天性静止性夜盲中无法检测到的S波视网膜电图b波。
Undetectable S cone electroretinogram b-wave in complete congenital stationary night blindness.
作者信息
Kamiyama M, Yamamoto S, Nitta K, Hayasaka S
机构信息
Department of Ophthalmology, Toyama Medical and Pharmaceutical University, Japan.
出版信息
Br J Ophthalmol. 1996 Jul;80(7):637-9. doi: 10.1136/bjo.80.7.637.
Abstract
AIMS
The short wavelength sensitive (S) cone electroretinograms (ERGs) were examined in two patients with the complete type of congenital stationary night blindness (CSNB).
METHODS
Ganzfeld spectral flashes in the presence of strong white adapting fields were used to elicit the S cone ERGs.
RESULTS
The S cone ERG b-wave was not detectable to short wavelength stimuli, while the mixed long (L) and middle (M) wavelength sensitive cone responses appeared normal in waveforms with normal amplitude in both patients. Both patients had normal colour vision on the Farnsworth Panel D-15.
CONCLUSIONS
These ERG results indicated that the S cone system as well as rod system is more impaired in complete CSNB than the L and M cone system and that normal colour vision may not depend on a normal S cone ERG to full field stimuli.
摘要
目的
对两名完全型先天性静止性夜盲（CSNB）患者的短波敏感（S）视锥细胞视网膜电图（ERG）进行检测。
方法
在强白色适应场存在的情况下，使用全视野光谱闪光来诱发S视锥细胞ERG。
结果
对于短波刺激，两名患者均未检测到S视锥细胞ERG的b波，而混合的长（L）波和中（M）波敏感视锥细胞反应在波形上正常，且振幅正常。两名患者在 Farnsworth Panel D - 15上的色觉均正常。
结论
这些ERG结果表明，在完全型CSNB中，S视锥细胞系统以及视杆细胞系统比L和M视锥细胞系统受损更严重，并且正常色觉可能不依赖于对全视野刺激的正常S视锥细胞ERG。
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