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完全性先天性静止性夜盲中无法检测到的S波视网膜电图b波。

Undetectable S cone electroretinogram b-wave in complete congenital stationary night blindness.

作者信息

Kamiyama M, Yamamoto S, Nitta K, Hayasaka S

机构信息

Department of Ophthalmology, Toyama Medical and Pharmaceutical University, Japan.

出版信息

Br J Ophthalmol. 1996 Jul;80(7):637-9. doi: 10.1136/bjo.80.7.637.

DOI:10.1136/bjo.80.7.637
PMID:8795377
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC505559/
Abstract

AIMS

The short wavelength sensitive (S) cone electroretinograms (ERGs) were examined in two patients with the complete type of congenital stationary night blindness (CSNB).

METHODS

Ganzfeld spectral flashes in the presence of strong white adapting fields were used to elicit the S cone ERGs.

RESULTS

The S cone ERG b-wave was not detectable to short wavelength stimuli, while the mixed long (L) and middle (M) wavelength sensitive cone responses appeared normal in waveforms with normal amplitude in both patients. Both patients had normal colour vision on the Farnsworth Panel D-15.

CONCLUSIONS

These ERG results indicated that the S cone system as well as rod system is more impaired in complete CSNB than the L and M cone system and that normal colour vision may not depend on a normal S cone ERG to full field stimuli.

摘要

目的

对两名完全型先天性静止性夜盲(CSNB)患者的短波敏感(S)视锥细胞视网膜电图(ERG)进行检测。

方法

在强白色适应场存在的情况下,使用全视野光谱闪光来诱发S视锥细胞ERG。

结果

对于短波刺激,两名患者均未检测到S视锥细胞ERG的b波,而混合的长(L)波和中(M)波敏感视锥细胞反应在波形上正常,且振幅正常。两名患者在 Farnsworth Panel D - 15上的色觉均正常。

结论

这些ERG结果表明,在完全型CSNB中,S视锥细胞系统以及视杆细胞系统比L和M视锥细胞系统受损更严重,并且正常色觉可能不依赖于对全视野刺激的正常S视锥细胞ERG。

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[Analysis of the human electroretinogram].[人类视网膜电图分析]
Ophthalmologica. 1952 Jun;123(6):396-413. doi: 10.1159/000301211.
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Nondetectable S-cone electroretinogram in a patient with crystalline retinopathy.结晶性视网膜病变患者的S锥体视网膜电图检测不到
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Autoantibodies against retinal bipolar cells in cutaneous melanoma-associated retinopathy.皮肤黑色素瘤相关性视网膜病变中针对视网膜双极细胞的自身抗体。
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S-cone function in patients with retinitis pigmentosa.色素性视网膜炎患者的S-视锥细胞功能
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The human S-cone electroretinogram and its variation among subjects with and without L and M-cone function.人类S视锥细胞视网膜电图及其在有和没有L和M视锥细胞功能的受试者中的变化。
Invest Ophthalmol Vis Sci. 1993 Jul;34(8):2437-42.
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Loss of electroretinographic oscillatory potentials, optic atrophy, and dysplasia in congenital stationary night blindness.先天性静止性夜盲症中的视网膜电图振荡电位丧失、视神经萎缩和发育异常。
Am J Ophthalmol. 1983 Oct;96(4):526-34. doi: 10.1016/s0002-9394(14)77917-6.
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The photopic electroretinogram in congenital stationary night blindness with myopia.伴有近视的先天性静止性夜盲症中的明视视网膜电图。
Invest Ophthalmol Vis Sci. 1983 Apr;24(4):442-50.
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Night blindness revisited: from man to molecules. Proctor lecture.夜盲症再探讨:从人类到分子。普罗克特讲座。
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Differential diagnosis of congenital tritanopia and dominantly inherited juvenile optic atrophy.先天性蓝色盲与显性遗传性青少年视神经萎缩的鉴别诊断。
Arch Ophthalmol. 1985 Oct;103(10):1496-501. doi: 10.1001/archopht.1985.01050100072022.
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Congenital stationary night blindness with negative electroretinogram. A new classification.伴有视网膜电图阴性的先天性静止性夜盲症。一种新的分类。
Arch Ophthalmol. 1986 Jul;104(7):1013-20. doi: 10.1001/archopht.1986.01050190071042.