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巴兰坦综合征的临床生物学特征及胎盘水肿的作用。

Clinical biological features of Ballantyne syndrome and the role of placental hydrops.

作者信息

Carbillon L, Oury J F, Guerin J M, Azancot A, Blot P

机构信息

Service de Gynécologie-Obstétrique, Hôpital Jean Verdier, Bondy, France.

出版信息

Obstet Gynecol Surv. 1997 May;52(5):310-4. doi: 10.1097/00006254-199705000-00023.

DOI:10.1097/00006254-199705000-00023
PMID:9140132
Abstract

Ballantyne syndrome was first described in association with severe hydrops fetalis caused by rhesus isoimmunization, and lately, in association with diverse etiologies of nonimmunological severe fetal hydrops. This report is a case of typical Ballantyne syndrome in association with lethal hydrops fetalis caused by Ebstein's anomaly. It is likely that any severe fetal hydrops with massive placental hydrops may produce Ballantyne syndrome. Hemodilution could be the main biological feature, differentiating Ballantyne syndrome from usual preeclamptic syndromes. Pathophysiological hypotheses are discussed.

摘要

巴兰坦综合征最初被描述为与恒河猴血型同种免疫引起的严重胎儿水肿相关,最近又被描述为与非免疫性严重胎儿水肿的多种病因相关。本报告是一例典型的巴兰坦综合征,与埃布斯坦畸形引起的致死性胎儿水肿相关。任何伴有大量胎盘水肿的严重胎儿水肿都可能导致巴兰坦综合征。血液稀释可能是巴兰坦综合征与常见先兆子痫综合征相鉴别的主要生物学特征。文中讨论了病理生理假说。

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