Weiss C, Willems S, Hofmann T, Rickers C, Meinertz T
Universitätsklinik Eppendorf, Abteilung für Kardiologie, Hamburg.
Med Klin (Munich). 1997 Jul 15;92(7):447-51. doi: 10.1007/BF03042579.
This case presents a 31-year-old male patient with anomalous origin of the left coronary artery from the pulmonary trunc. First symptom of the disease was a survived sudden cardiac death. Subsequent angiographic and echocardiographic studies demonstrated the anomalous origin of the left coronary artery from the pulmonary artery. There were no signs of prior myocardial infarction. After reimplantation of the anomalous originating left coronary artery no myocardial ischemia could be detected in the thallium-201 myocardial imaging, which was present before surgical correction. In this case myocardial ischemia was the only potential triggering mechanism responsible for the sudden cardiac death, which was no longer detectable after surgical correction. Therefore no additional pharmacological and nonpharmacological antiarrhythmic treatment was initiated.
In rare cases the first manifestation of Bland White Garland syndrome in the adult patient could be sudden cardiac death due to ventricular fibrillation.
该病例为一名31岁男性患者,左冠状动脉起源于肺动脉干异常。该疾病的首发症状是一次心脏性猝死幸存。随后的血管造影和超声心动图研究证实左冠状动脉起源于肺动脉异常。无既往心肌梗死迹象。在对异常起源的左冠状动脉进行再植入术后,在手术矫正前存在的铊-201心肌显像中未检测到心肌缺血。在该病例中,心肌缺血是导致心脏性猝死的唯一潜在触发机制,手术矫正后不再可检测到。因此未启动额外的药物和非药物抗心律失常治疗。
在罕见情况下,成人患者布兰德·怀特·加兰综合征的首发表现可能是因室颤导致的心脏性猝死。