Hung C C, Tu Y K, Su C F, Lin L S, Shih C J
Department of Neurosurgery, National Taiwan University Hospital, Taipei, ROC.
Clin Neurol Neurosurg. 1997 Oct;99 Suppl 2:S23-5. doi: 10.1016/s0303-8467(97)00036-x.
From January 1978 to December 1995, 92 cases of Moyamoya disease were collected from seven major medical centers in Taiwan. The data gave an annual incidence rate of 0.048 per 100,000 population. There were 40 males and 52 females and the ages ranged from 2 to 62 years with the peak incidence in the 31-40 year age group (23 cases). Cerebral infarction occurred in 20 out of 24 juvenile patients (83%), and in 24 out of 68 adult patients (35%). The difference was statistically significant. Haemorrhagic stroke was more frequent in adult patients. Computed tomographic scans following stroke showed cerebral infarction in 44 cases, ventricular haemorrhage in 26 cases, intracerebral haemorrhage in 14 cases and pure subarachnoid haemorrhage in eight. The most frequent initial symptom was motor disturbance (59%), followed by headache (49%) and impaired consciousness (35%). This survey showed an incidence rate much lower than that in Japan, but comparable with those in other Oriental countries and higher than those in Western countries. The male-to-female ratio once differed considerably from that of the Japanese series, but from the present study is now quite similar.
1978年1月至1995年12月，从台湾的七个主要医疗中心收集了92例烟雾病病例。数据显示年发病率为每10万人0.048例。其中男性40例，女性52例，年龄范围为2至62岁，发病高峰在31 - 40岁年龄组（23例）。24例青少年患者中有20例发生脑梗死（83%），68例成年患者中有24例发生脑梗死（35%）。差异具有统计学意义。出血性卒中在成年患者中更为常见。卒中后的计算机断层扫描显示，44例为脑梗死，26例为脑室出血，14例为脑内出血，8例为单纯蛛网膜下腔出血。最常见的初始症状是运动障碍（59%），其次是头痛（49%）和意识障碍（35%）。这项调查显示发病率远低于日本，但与其他东方国家相当，高于西方国家。男女比例曾与日本系列有很大差异，但目前本研究中的比例与日本相当接近。
