Della Rossa A, Tavoni A, Tognetti A, Testi C, Bombardieri S
Clinical Immunology Unit, University of Pisa, Italy.
Clin Rheumatol. 1998;17(6):515-7. doi: 10.1007/BF01451290.
Myelodysplastic syndromes (MDS) are hematologic disorders characterised by peripheral cytopenias and the hystologic features of hematologic dysplasia. Their association with autoimmune manifestations have been suggested by several authors: recently, the appearance of Behçet's disease during MDS has been reported. We describe the occurrence of MDS in a patient affected by Behçet's syndrome with gastrointestinal involvement and congenital panhypopituitarism.
骨髓增生异常综合征(MDS)是一种血液系统疾病,其特征为外周血细胞减少以及血液发育异常的组织学特征。几位作者都曾提出过它们与自身免疫表现之间的关联:最近,已有报道称在MDS期间出现了白塞病。我们描述了一名患有白塞综合征且有胃肠道受累及先天性全垂体功能减退的患者发生MDS的情况。