Khan I U, Bhol K C, Ahmed A R
Department of Medicine, New England Baptist Hospital, The Center for Blood Research, Harvard Medical School, Boston, MA 02115, USA.
J Am Acad Dermatol. 1999 Mar;40(3):485-8. doi: 10.1016/s0190-9622(99)70504-9.
Linear IgA bullous dermatosis is a blistering disease with a heterogeneous clinical manifestation, characterized by deposition of IgA along the basement membrane zone of perilesional skin on direct immunofluorescence. We describe a patient with chronic renal failure who experienced linear IgA bullous dermatosis. Long-term administration of intravenous immunoglobulin therapy was associated with clinical remission lasting more than 12 months.
线状IgA大疱性皮病是一种临床表现多样的水疱性疾病，其特征为在直接免疫荧光检查下，IgA沿皮损周围皮肤的基底膜带沉积。我们描述了一名患有慢性肾衰竭并罹患线状IgA大疱性皮病的患者。长期静脉注射免疫球蛋白治疗与持续超过12个月的临床缓解相关。
