Oh S J, Joy J L, Kuruoglu R
Department of Neurology, University of Alabama, Birmingham 35294.
J Neurol Neurosurg Psychiatry. 1992 Aug;55(8):677-80. doi: 10.1136/jnnp.55.8.677.
The clinical electrophysiological and histological features of 10 cases of "chronic sensory demyelinating neuropathy" (CSDN) are reported. This entity is characterised by: 1) subacute or chronic progression; 2) pure sensory neuropathy; 3) high spinal fluid protein in the majority of cases; 4) electrophysiological evidence of demyelination affecting motor as well as sensory nerve fibres; 5) demyelination on sural nerve biopsy and 6) good response to immunotherapy in progressive phase. It is believed that this entity represents chronic inflammatory demyelinating polyneuropathy (CIDP) presenting as pure sensory neuropathy.
报告了10例“慢性感觉性脱髓鞘性神经病”（CSDN）的临床电生理和组织学特征。该病症的特点为：1）亚急性或慢性进展；2）纯感觉性神经病；3）大多数病例脑脊液蛋白含量高；4）电生理证据表明脱髓鞘影响运动及感觉神经纤维；5）腓肠神经活检显示脱髓鞘；6）进展期对免疫治疗反应良好。据信该病症代表表现为纯感觉性神经病的慢性炎症性脱髓鞘性多发性神经病（CIDP）。
