Enriquez G, Lucaya J, Allende E, Garcia-Peña P
Radiology Department, Hospital Infantil Vall d'Hebron, Barcelona, Spain.
Pediatr Radiol. 1992;22(4):283-6. doi: 10.1007/BF02019861.
Intrahepatic biliary stones in seven non-Oriental patients were studied in all by sonography, in four patients by computed tomography and in four patients by percutaneous transhepatic cholangiography. For patients had extrahepatic biliary atresia treated with portoenterostomies, one patient had undergone partial liver transplantation and of the remaining two, one had cystic fibrosis and the other immunodeficiency syndrome. All sonograms were abnormal and showed echogenic foci within the liver, with or without associated signs of biliary tract dilatation. CT confirmed the biliary tract dilatation yet calculi were identified in one patient only. PTC was particularly helpful in the patient with immunodeficiency in whom features typical of sclerosing cholangitis were found. This report emphasizes the variable radiological appearance of bile stones which to our knowledge have rarely been described in children with entities other than Oriental cholangitis.
我们对7名非东方患者的肝内胆管结石进行了全面研究,其中4名患者接受了计算机断层扫描,4名患者接受了经皮经肝胆管造影。对于接受了肝门空肠吻合术治疗的肝外胆管闭锁患者,1例接受了部分肝移植,其余2例中,1例患有囊性纤维化,另1例患有免疫缺陷综合征。所有超声检查结果均异常,显示肝脏内有回声灶,伴有或不伴有胆道扩张的相关体征。CT证实了胆道扩张,但仅在1例患者中发现结石。经皮经肝胆管造影对患有免疫缺陷的患者特别有帮助,在该患者中发现了典型的硬化性胆管炎特征。本报告强调了胆石症的可变放射学表现,据我们所知,除东方胆管炎外,胆石症在其他疾病的儿童中很少被描述。