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一位年轻女性患乳糜泻危象并伴有低钾性麻痹。

Celiac crisis with hypokalemic paralysis in a young lady.

作者信息

Gupta Tarun, Mandot Ameet, Desai Devendra, Abraham Philip, Joshi Anand

机构信息

Division of Gastroenterology, P D Hinduja Hospital and Medical Research Center, Mumbai 400 016, India.

出版信息

Indian J Gastroenterol. 2006 Sep-Oct;25(5):259-60.

PMID:17090849
Abstract

Celiac crisis presents as severe acute diarrhea with life-threatening metabolic derangement in a patient with celiac disease. We report a 30-year-old lady who was admitted with one-month history of worsening small bowel-type diarrhea. She developed acute quadriparesis due to refractory hypokalemia. Celiac disease was diagnosed on the basis of positive serology and histological features. She improved with aggressive correction of hypokalemia and gluten-free diet. Celiac crisis is a rare presentation of this heterogeneous disease in adulthood.

摘要

乳糜泻危象表现为患有乳糜泻的患者出现严重急性腹泻并伴有危及生命的代谢紊乱。我们报告一名30岁女性,因小肠型腹泻恶化1个月入院。她因难治性低钾血症出现急性四肢瘫。根据血清学阳性和组织学特征诊断为乳糜泻。通过积极纠正低钾血症和无麸质饮食,她的病情有所改善。乳糜泻危象是这种异质性疾病在成年期的一种罕见表现。

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Celiac crisis with hypokalemic paralysis in a young lady.一位年轻女性患乳糜泻危象并伴有低钾性麻痹。
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引用本文的文献

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Life-threatening onset of coeliac disease: a case report and literature review.危及生命的乳糜泻发病:病例报告及文献复习。
BMJ Open Gastroenterol. 2020 May;7(1). doi: 10.1136/bmjgast-2020-000406.
2
Celiac Crisis in a Young Woman: Raising Awareness of a Life-Threatening Condition.一名年轻女性的乳糜泻危象:提高对一种危及生命病症的认识
Middle East J Dig Dis. 2019 Oct;11(4):230-233. doi: 10.15171/mejdd.2019.154. Epub 2019 Nov 5.
3
Celiac crisis, a rare occurrence in adult celiac disease: A systematic review.乳糜泻危象,成人乳糜泻中的罕见情况:一项系统综述
World J Clin Cases. 2019 Feb 6;7(3):311-319. doi: 10.12998/wjcc.v7.i3.311.
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Hypokalemic paraparesis: Presenting feature of previously undiagnosed celiac disease in celiac crisis.低钾性轻瘫:乳糜泻危象中既往未诊断的乳糜泻的表现特征。
Indian J Crit Care Med. 2015 Aug;19(8):501. doi: 10.4103/0972-5229.162478.
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Celiac crisis presenting with status epilepticus and encephalopathy.以癫痫持续状态和脑病为表现的乳糜泻危象。
Eur J Pediatr. 2014 Dec;173(12):1561-4. doi: 10.1007/s00431-013-2097-1. Epub 2013 Jul 31.
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Celiac crisis with ataxia in a child.一名患有共济失调的儿童出现乳糜泻危象。
Clinics (Sao Paulo). 2011;66(1):173-5. doi: 10.1590/s1807-59322011000100031.
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Celiac crisis is a rare but serious complication of celiac disease in adults.乳糜泻危象是成人乳糜泻的一种罕见但严重的并发症。
Clin Gastroenterol Hepatol. 2010 Jul;8(7):587-90. doi: 10.1016/j.cgh.2010.04.009. Epub 2010 Apr 24.
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Can J Gastroenterol. 2008 Jun;22(6):574-6. doi: 10.1155/2008/453520.