Aggarwal Amitesh, Sinha Bineet, Rajpal Surender, Dwivedi Shridhar, Sharma Vishal
Department of Medicine/ Preventive Cardiology, University College of Medical Sciences, University of Delhi & GTB Hospital, Delhi-110095.
Indian Pacing Electrophysiol J. 2009 Nov 1;9(6):360-3.
Endomyocardial fibrosis is a progressive disease of unknown origin affecting children and young adults. It involves inflow portion of right and/or left ventricle and apex. It may be associated with thrombus. Literature regarding right ventricular endomyocardial fibrosis with thrombus is scarce. Here we report a rare case of right ventricular endomyocardial fibrosis presenting as ventricular tachycardia and echocardiographic evidence of apical thrombus. Interestingly there was no pulmonary involvement or evidence of deep venous thrombosis. This case also underscores the importance of urgent echocardiography in diagnosis of obscure cases of ventricular tachycardia.
心内膜心肌纤维化是一种病因不明的进行性疾病,影响儿童和年轻人。它累及右心室和/或左心室的流入部分以及心尖。它可能与血栓有关。关于伴有血栓的右心室心内膜心肌纤维化的文献很少。在此,我们报告一例罕见的右心室心内膜心肌纤维化病例,表现为室性心动过速,且超声心动图显示心尖有血栓形成。有趣的是,该病例无肺部受累或深静脉血栓形成的证据。该病例还强调了急诊超声心动图在诊断不明原因室性心动过速病例中的重要性。