Chagas Disease Multidisciplinary Research Laboratory, University of Brasilia, Federal District, Brazil.
Clin Microbiol Rev. 2011 Jul;24(3):592-630. doi: 10.1128/CMR.00063-10.
Acute Trypanosoma cruzi infections can be asymptomatic, but chronically infected individuals can die of Chagas' disease. The transfer of the parasite mitochondrial kinetoplast DNA (kDNA) minicircle to the genome of chagasic patients can explain the pathogenesis of the disease; in cases of Chagas' disease with evident cardiomyopathy, the kDNA minicircles integrate mainly into retrotransposons at several chromosomes, but the minicircles are also detected in coding regions of genes that regulate cell growth, differentiation, and immune responses. An accurate evaluation of the role played by the genotype alterations in the autoimmune rejection of self-tissues in Chagas' disease is achieved with the cross-kingdom chicken model system, which is refractory to T. cruzi infections. The inoculation of T. cruzi into embryonated eggs prior to incubation generates parasite-free chicks, which retain the kDNA minicircle sequence mainly in the macrochromosome coding genes. Crossbreeding transfers the kDNA mutations to the chicken progeny. The kDNA-mutated chickens develop severe cardiomyopathy in adult life and die of heart failure. The phenotyping of the lesions revealed that cytotoxic CD45, CD8(+) γδ, and CD8α(+) T lymphocytes carry out the rejection of the chicken heart. These results suggest that the inflammatory cardiomyopathy of Chagas' disease is a genetically driven autoimmune disease.
急性克氏锥虫感染可能无症状,但慢性感染个体可能死于恰加斯病。寄生虫线粒体动基体 DNA(kDNA)小环转移到恰加斯病患者的基因组中可以解释疾病的发病机制;在明显伴有心肌病的恰加斯病中,kDNA 小环主要整合到几个染色体的逆转录转座子中,但小环也存在于调节细胞生长、分化和免疫反应的基因的编码区。通过对鸡模型系统进行跨物种分析,可以准确评估基因型改变在恰加斯病自身组织自身免疫排斥中的作用,该模型系统对克氏锥虫感染具有抗性。在孵化前将克氏锥虫接种到鸡胚中会产生无寄生虫的雏鸡,这些雏鸡主要保留在大染色体编码基因中的 kDNA 小环序列。杂交会将 kDNA 突变转移到鸡后代中。kDNA 突变鸡在成年后会发展出严重的心肌病并死于心力衰竭。病变的表型分析表明,细胞毒性 CD45、CD8(+)γδ 和 CD8α(+)T 淋巴细胞对鸡心脏进行排斥。这些结果表明,恰加斯病的炎症性心肌病是一种遗传驱动的自身免疫性疾病。