Kala Chayanika, Agarwal Asha, Kala Sanjay
Departments of Pathology, G.S.V.M. Medical College, Kanpur, India.
J Cytol. 2011 Jul;28(3):131-3. doi: 10.4103/0970-9371.83473.
Rosai-Dorfman disease, that is, sinus histiocytosis with massive lymphadenopathy is a benign systemic proliferative disorder of histiocytes. The typical clinical presentation of the disease includes bilateral painless massive lymphadenopathy, fever and polyclonal hypergammaglobulinemia. Extranodal involvement is present in only a few cases and skin lesions are the most common form of extranodal disease. However, purely cutaneous Rosai-Dorfman disease is uncommon. In this study, we describe a 10-year-old child presenting with bilateral ocular involvement.
罗萨伊-多夫曼病，即伴有巨大淋巴结病的窦性组织细胞增多症，是一种组织细胞的良性全身性增殖性疾病。该疾病的典型临床表现包括双侧无痛性巨大淋巴结病、发热和多克隆高球蛋白血症。仅少数病例存在结外受累，皮肤病变是结外疾病最常见的形式。然而，单纯皮肤型罗萨伊-多夫曼病并不常见。在本研究中，我们描述了一名出现双侧眼部受累的10岁儿童。
