Kwak Hyun Jung, Moon Ji-Yong, Kim Sa-Il, Kim Tae Hyung, Sohn Jang Won, Kim Sang-Heon, Shin Dong Ho, Park Sung Soo, Chung Won Sang, Yoon Ho Joo
Department of Internal Medicine, Hanyang University College of Medicine, Seoul, Korea.
Tuberc Respir Dis (Seoul). 2012 Jun;72(6):501-6. doi: 10.4046/trd.2012.72.6.501. Epub 2012 Jun 29.
Congenital cystic adenomatoid malformation (CCAM) is an uncommon, nonhereditary anomaly caused by arrest of lung. Patients with CCAM may present with respiratory distress as newborns, or may remain asymptomatic until later in life. CCAM type I is rarely found in association with bronchial atresia (BA) in adults; we present such a case.
A 54-year-old female presented with chronic cough and blood-tinged sputum. Physical examination and laboratory tests were unremarkable. Chest radiographs and a CT scan of the chest showed multiple large air-filled cysts consistent with a CCAM in the right lower lobe, and an oval-shaped opacity in the distal right middle lobal bronchus. Based on the radiologic findings, right middle lobectomy and a medial basal segmentectomy of the right lower lobe were performed via a thoracotomy. These lesions were consistent with Stocker's Type I CCAM and BA in the different lobes.
先天性囊性腺瘤样畸形（CCAM）是一种由肺发育停滞引起的罕见非遗传性异常。CCAM患者在新生儿期可能出现呼吸窘迫，也可能直到生命后期仍无症状。I型CCAM在成人中很少与支气管闭锁（BA）相关联；我们报告这样一例病例。
一名54岁女性出现慢性咳嗽和痰中带血。体格检查和实验室检查无异常。胸部X线片和胸部CT扫描显示右肺下叶有多个与CCAM相符的大的含气囊肿，右肺中叶远端支气管有一个椭圆形致密影。根据影像学表现，通过开胸手术进行了右肺中叶切除术和右肺下叶内侧基底段切除术。这些病变在不同肺叶符合斯托克I型CCAM和BA。
