Ratra Dhanashree, Raval Vishal
Department of Vitreoretinal Services, Bhagawan Mahavir Medical Research Foundation, Sankara Nethralaya, Chennai, Tamil Nadu, India.
Oman J Ophthalmol. 2013 May;6(2):112-5. doi: 10.4103/0974-620X.116648.
Macular hole (MH) is uncommonly seen in association with retinitis pigmentosa (RP), optic disc pit or choroidal coloboma. The visual disability in eyes with RP, optic disc pit or choroidal coloboma can range from mild to severe. However, the macula may not be involved in the primary pathology and hence, the central vision may be preserved in these eyes. If a MH develops in such eyes the central vision is lost, making the patient severely vision disabled. A perceived poor prognosis in such patients may lead to no intervention. However, an attempt should be made to repair and restore the macula in these situations in order to conserve the vision and limit disability. These eyes can however pose unique surgical challenges. We report our experiences of operating on cases of MH associated with unusual concomitant pathologies such as RP, choroidal coloboma, and optic pit. The outcomes and the surgical challenges differed greatly from the conventional idiopathic MH surgery.
黄斑裂孔（MH）罕见与视网膜色素变性（RP）、视盘凹陷或脉络膜缺损同时出现。患有RP、视盘凹陷或脉络膜缺损的眼睛的视力残疾程度可从轻度到重度不等。然而，黄斑可能未参与原发性病变，因此，这些眼睛的中心视力可能得以保留。如果在这类眼睛中发生了MH，中心视力就会丧失，使患者严重视力残疾。这类患者被认为预后不佳可能导致不进行干预。然而，在这些情况下应尝试修复和恢复黄斑，以保护视力并限制残疾。不过，这些眼睛可能会带来独特的手术挑战。我们报告了对与RP、脉络膜缺损和视盘凹陷等不寻常伴随病变相关的MH病例进行手术的经验。其结果和手术挑战与传统的特发性MH手术有很大不同。
