Yih Ng Deborah Chieh, Chyen Lee Hwee, Cunli Yang, Jaywantraj Punamiya Sundeep, Isip Azucena Benedict Cesar, Anil Sule Ashish
Department of General Medicine, Tan Tock Seng Hospital, Singapore ; Department of General Surgery, Tan Tock Seng Hospital, Singapore.
Department of General Medicine, Tan Tock Seng Hospital, Singapore.
Int J Angiol. 2014 Mar;23(1):71-6. doi: 10.1055/s-0033-1348883.
The nutcracker syndrome is a rare clinical manifestation of symptoms caused by the compression of the left renal vein by an overriding superior mesenteric artery, an anatomical variant otherwise known as the nutcracker phenomenon. Usually present in women and children, when symptomatic, it commonly presents with hematuria, proteinuria, and chronic pelvic pain. Effective modalities of treatment apart from conservative management, include both invasive surgical procedures such as renal vein transposition and autotransplantation of the kidney and more popular recently, the less invasive endovascular stenting. Both options, however, are not without complications, such as, retroperitoneal hematomas or stent migration, thrombosis and restenosis. We now present a case of spontaneous renosplenic shunting in a 68-year-old lady of Chinese descent with the nutcracker syndrome-the first of such cases to be ever reported in a patient with no preexisting predilection for chronic liver disease and portosystemic shunting. Despite having significant pelvic venous congestion as evident on computed tomography scans, she remained asymptomatic. This may present a novel paradigm shift for the treatment of the nutcracker syndrome -surgical creation of a renosplenic bypass instead of current modalities, an alternative solution which can be performed laparoscopically and is without problems related to stent use. The creation of laparoscopic splenorenal bypass has been reported once thus far in Cleveland Ohio by Chung and Gill with good symptomatic improvement but no further studies since to validate its long-term effectiveness.
胡桃夹综合征是一种罕见的临床表现,由肠系膜上动脉压迫左肾静脉所致,这种解剖变异也被称为胡桃夹现象。该综合征通常见于女性和儿童,有症状时,常见表现为血尿、蛋白尿和慢性盆腔疼痛。除保守治疗外,有效的治疗方式包括侵入性外科手术,如肾静脉转位术和肾脏自体移植术,以及近年来更常用的创伤较小的血管内支架置入术。然而,这两种选择都并非没有并发症,如腹膜后血肿、支架移位、血栓形成和再狭窄。我们现在报告一例68岁华裔女性胡桃夹综合征患者出现自发性脾肾分流的病例,这是首例在无慢性肝病和门体分流倾向的患者中报道的此类病例。尽管计算机断层扫描显示盆腔静脉明显淤血,但她仍无症状。这可能为胡桃夹综合征的治疗带来一种新的模式转变——通过手术创建脾肾分流,而非采用目前的治疗方式,这是一种可通过腹腔镜进行且不存在与支架使用相关问题的替代解决方案。到目前为止,俄亥俄州克利夫兰市的钟和吉尔曾报道过一例腹腔镜脾肾分流术,症状有明显改善,但此后没有进一步研究来验证其长期有效性。