Aggressive angiomyxoma in pregnancy.

Aggressive angiomyxoma is a locally aggressive soft tissue tumour mainly arises from perineal, vulval and bladder connective tissue. As it has a tendency for local infiltration and recurrence so long-term follow-up and treatment is required. A case of 24 years old primigravida, 16 weeks pregnant with huge pedunculated lobulated growth arising from right labia majora for the last one month is presented. There was a rapid increase in the size of tumour up to 30 x 26 cm and weight of 18 kg with in a month. The growth was excised with wide margins and tissues sent for histopathology to be diagnosed as an aggressive angiomyxoma. Postoperatively, no chemo or radiotherapy was given. She was regularly followed-up and presented in the 37th week of pregnancy with ruptured membranes and failure of progress of labour. Her caesarean section was done and baby boy delivered. She had a regular follow-up and conceived again after 3 years. No recurrence of the growth has occurred within 5 years.