Karagiannis Dimitrios, Kontadakis Georgios A, Kandarakis Artemios S, Markomichelakis Nikolaos, Georgalas Ilias, Parikakis Efstratios A, Kabanarou Stamatina A
Ophthalmiatreio Eye Hospital of Athens, Eleftheriou Venizelou 26, 106 72 Athens, Greece.
Department of Ophthalmology, General Hospital of Athens, Leoforos Mesogion 154, 115 27 Athens, Greece.
Case Rep Med. 2014;2014:290696. doi: 10.1155/2014/290696. Epub 2014 Jul 21.
Background. To report a case of acute zonal occult outer retinopathy (AZOOR) with atypical electrophysiology findings. Case Presentation. A 23-year-old-female presented with visual acuity deterioration in her right eye accompanied by photopsia bilaterally. Corrected distance visual acuity at presentation was 20/50 in the right eye and 20/20 in the left eye. Fundus examination was unremarkable. Visual field (VF) testing revealed a large scotoma. Pattern and full-field electroretinograms (PERG and ERG) revealed macular involvement associated with generalized retinal dysfunction. Electrooculogram (EOG) light rise and the Arden ratio were within normal limits bilaterally. The patient was diagnosed with AZOOR due to clinical findings, visual field defect, and ERG findings. Conclusion. This is a case of AZOOR with characteristic VF defects and clinical symptoms presenting with atypical EOG findings.
背景。报告一例具有非典型电生理检查结果的急性区域性隐匿性外层视网膜病变(AZOOR)。病例报告。一名23岁女性因右眼视力下降伴双侧闪光感就诊。就诊时右眼矫正远视力为20/50,左眼为20/20。眼底检查未见明显异常。视野(VF)检查显示有一个大的暗点。图形和全视野视网膜电图(PERG和ERG)显示黄斑受累并伴有广泛性视网膜功能障碍。双眼眼电图(EOG)光峰和Arden比值均在正常范围内。根据临床表现、视野缺损和ERG检查结果,该患者被诊断为AZOOR。结论。这是一例具有特征性视野缺损和临床症状且伴有非典型EOG检查结果的AZOOR病例。