Cisse Mouhamadou Moustapha, Seck Sidy Mohamed, Oumar Daher Abdoul Karim, Fall Khodia, Lemrabott Ahmed Tall, Diallo Moussa, Faye Maria, Faye Moustapha, Niang Abdou, Diouf Boucar
Nephrology Department of Teaching Hospital, Aristide le Dantec, Dakar, Sénégal.
Nephrology Department of Gaston Berger University, Saint Louis, Sénégal.
Pan Afr Med J. 2015 May 22;21:46. doi: 10.11604/pamj.2015.21.46.6344. eCollection 2015.
Scleroderma renal crisis (SRC) is defined as the new onset of accelerated arterial hypertension and /or rapidly progressive oliguric renal failure during the course of systemic sclerosis. It is a rare but life-threatening complication. This formerly serious complication has got a considerable brighter outlook since the introduction of angiotensin converting enzyme inhibitors (ACE) however the mortality is still remaining high. We report two cases of SRC which to our knowledge are the firsts described in Dakar. They were two women aged 45 and 32 years, one of them was previously following for systemic sclerosis. Both of them had malignant hypertension associated with rapidly progressive renal failure, the other was put under corticosteroid therapy four months before SRC occurrence. The histological and laboratory finding showed thrombotic microangiopathy. The height blood pressure returned to normal value after treatment with ACE inhibitors. The final outcome was undesirable with the death of one after two months due to the hemodialysis discontinuation and persistence of renal failure in the other.
硬皮病肾危象(SRC)被定义为在系统性硬化症病程中出现的新发加速性动脉高血压和/或快速进展的少尿性肾衰竭。它是一种罕见但危及生命的并发症。自从引入血管紧张素转换酶抑制剂(ACE)以来,这种以前严重的并发症有了相当光明的前景,然而死亡率仍然很高。我们报告两例SRC病例,据我们所知,这是在达喀尔首次描述的病例。她们是两名年龄分别为45岁和32岁的女性,其中一人之前患有系统性硬化症。她们都患有恶性高血压并伴有快速进展的肾衰竭,另一人在SRC发生前四个月接受了皮质类固醇治疗。组织学和实验室检查结果显示为血栓性微血管病。用ACE抑制剂治疗后,高血压恢复到正常水平。最终结果不理想,其中一人在两个月后因停止血液透析死亡,另一人则持续存在肾衰竭。