Dokania Vivek, Rajguru Anagha, Kaur Harmanjot, Agarwal Ketan, Kanetkar Sujata, Thakur Prajakta, Patel Femina, Shukla Dhirajkumar
Department of ENT, Krishna Institute of Medical Sciences Deemed University, Karad 415110, India.
Wyckoff Heights Medical Center, Brooklyn, NY 11237, USA.
Case Rep Otolaryngol. 2017;2017:1061958. doi: 10.1155/2017/1061958. Epub 2017 May 24.
Cystic hygroma (CH) is a benign infiltrative malformation of the lymphatic channels. We report a case of a 28-year-old Indian female who presented with rapidly enlarging right sided neck swelling over the posterior triangle since 5 days. Complete resection of CH is sometimes not amenable because of its infiltrative nature and involvement of surrounding vital structures. However, in our patient successful complete surgical resection was undertaken. The MRI findings of our patient were consistent with brachial cleft cyst; this posed a challenge in the diagnosis of CH. The histopathological analysis of the resected mass confirmed CH. CH is rare in adults and such an acute presentation is exceptionally atypical. History of prior trauma and infection are known etiological factors for adult CH; these were conspicuously absent in our patient. CH should be considered in the differentials of rapidly enlarging cystic swelling of posterior region of neck in adults. Optimal and timely management is necessary to achieve a favorable prognosis. Therefore, we report a case of rapidly enlarging cervical CH in an adult along with extensive literature review to have a better understanding regarding epidemiology, etiopathogenesis, clinical presentation, optimal management, and prognosis of such a rare entity in adults.
囊状水瘤(CH)是一种淋巴管的良性浸润性畸形。我们报告一例28岁的印度女性病例,该患者自5天前起右侧颈后三角区出现迅速增大的颈部肿胀。由于CH具有浸润性且累及周围重要结构,有时无法进行完整切除。然而,我们的患者成功进行了完整的手术切除。我们患者的磁共振成像(MRI)表现与鳃裂囊肿一致;这给CH的诊断带来了挑战。切除肿块的组织病理学分析证实为CH。CH在成人中罕见,如此急性的表现极为不典型。既往创伤和感染史是成人CH已知的病因;我们的患者明显不存在这些因素。成人颈部后方迅速增大的囊性肿胀的鉴别诊断中应考虑CH。为获得良好预后,进行最佳且及时的治疗很有必要。因此,我们报告一例成人颈部迅速增大的CH病例,并进行广泛的文献综述,以便更好地了解这种成人罕见疾病的流行病学、病因发病机制、临床表现、最佳治疗及预后。