Saviour Mary Jacqueline, Hassan Sam
Mediclinic City Hospital, Dubai Health Care City, Dubai, United Arab Emirates.
Pediatr Rep. 2017 Jun 26;9(2):7163. doi: 10.4081/pr.2017.7163.
Kawasaki disease (KD) is an acute febrile vasculitis of an unknown cause. It affects children <5 year of age, even if cases over 5 years old have been also reported. It is the commonest cause of acquired heart diseases in children which may lead to serious morbidity and mortality. The complications and mortality increase when the diagnosis is delayed. One of the main reasons leading to delayed diagnosis and consequent delayed treatment is the unusual presentation of KD. Its unusual manifestations have been increasingly reported to jeopardize the timely diagnosis and proper treatment. As there is not yet available blood test to diagnose it, low threshold should be taken into account for considering KD, when the clinical criteria are not typical. KD with renal manifestations is infrequently described. We present and discuss a case of an unusual presentation of KD presenting as bloody diarrhea and acute renal failure.
川崎病(KD)是一种病因不明的急性发热性血管炎。它主要影响5岁以下儿童,不过也有5岁以上病例的报道。它是儿童后天性心脏病最常见的病因,可能导致严重的发病和死亡。诊断延迟会增加并发症和死亡率。导致诊断延迟及随之而来的治疗延迟的主要原因之一是KD的不寻常表现。越来越多报道称其不寻常表现会危及及时诊断和恰当治疗。由于尚无血液检测手段来诊断该病,当临床标准不典型时,考虑KD应保持较低阈值。KD合并肾脏表现的情况鲜有描述。我们呈现并讨论一例以血性腹泻和急性肾衰竭为表现的不寻常KD病例。