Patel Jay A, Piper James B, Wang Brant G
Virginia Commonwealth University School of Medicine, Inova Fairfax Hospital, Falls Church, Virginia, USA.
Department of Surgery, Inova Fairfax Hospital, Falls Church, Virginia, USA.
BMJ Case Rep. 2018 Feb 8;2018:bcr-2017-223232. doi: 10.1136/bcr-2017-223232.
Follicular dendritic cell (FDC) sarcoma is a very rare neoplasm which commonly involves the lymph nodes and less commonly involves extranodal organs such as the liver. Most cases of FDC sarcoma are idiopathic, however some cases are associated with other disease states. Management of FDC sarcoma is primarily focused on surgical resection of the mass, and secondarily focused on radiotherapy, chemotherapy and/or biologic pharmacotherapy. We report the case of a patient who was found to have FDC sarcoma presenting as an obstructing mass of the porta hepatis, a manifestation which does not appear to be reported in the literature.
滤泡树突状细胞（FDC）肉瘤是一种非常罕见的肿瘤，通常累及淋巴结，较少累及肝等结外器官。大多数FDC肉瘤病例是特发性的，然而一些病例与其他疾病状态相关。FDC肉瘤的治疗主要集中于手术切除肿块，其次是放疗、化疗和/或生物药物治疗。我们报告一例患者，其被发现患有表现为肝门部梗阻性肿块的FDC肉瘤，这种表现似乎未见文献报道。
