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脂膜炎、胰腺炎和多关节炎:一种罕见的临床综合征。

Panniculitis, pancreatitis, and polyarthritis: a rare clinical syndrome.

作者信息

Graham Paul M, Altman David A, Gildenberg Stuart R

机构信息

Department of Dermatology, Saint Joseph Mercy Hospital System, Ypsilanti, Michigan, USA.

Midwest Center for Dermatology and Cosmetic Surgery, St. John Macomb-Oakland Hospital, Warren, Michigan, USA.

出版信息

Cutis. 2018 Jan;101(1):E34-E37.

PMID:29529121
Abstract

A rare triad composed of lobular panniculitis in the setting of pancreatitis and polyarthritis is termed panniculitis, pancreatitis, and polyarthritis (PPP) syndrome. Pancreatic panniculitis is a rare form of subcutaneous fat necrosis associated with underlying pancreatic disease. We describe a case of PPP syndrome and review the relevant literature associated with this rare clinical syndrome. Despite numerous adjuvant therapies, definitive treatment of PPP syndrome requires correction of the underlying pancreatic disease.

摘要

一种罕见的三联征,由胰腺炎和多关节炎背景下的小叶性脂膜炎组成,被称为脂膜炎、胰腺炎和多关节炎(PPP)综合征。胰腺性脂膜炎是一种与潜在胰腺疾病相关的罕见的皮下脂肪坏死形式。我们描述了一例PPP综合征病例,并回顾了与这种罕见临床综合征相关的文献。尽管有多种辅助治疗方法,但PPP综合征的确定性治疗需要纠正潜在的胰腺疾病。

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