威尔斯综合征——一段历程
Wells Syndrome - An Odyssey.
作者信息
Heinig Birgit, Vojvocic Aleksandra, Lotti Torello, Tirant Michael, Wollina Uwe
机构信息
Center of Physical and Rehabilitative Medicine, Städtisches Klinikum Dresden, Academic Teaching Hospital, Dresden, Germany.
Military Medical Academy of Belgrade, Belgrade, Serbia.
出版信息
Open Access Maced J Med Sci. 2019 Jun 30;7(18):3002-3005. doi: 10.3889/oamjms.2019.572. eCollection 2019 Sep 30.
BACKGROUND
Wells syndrome is a rare idiopathic dermatosis of the eosinophilic spectrum. Diagnostic criteria include cutaneous eruptions of variable morphology with eosinophilic infiltrates, peripheral blood eosinophilia, a relapsing, remitting course, and exclusion of systemic disease. Diagnosis is often delayed.
CASE PRESENTATION
We present a 28-year older man with recently developed pruritic and sometimes painful erythema. His medical history was positive for coughing in the evening that started in November 2012. Later, a pansinusitis developed. Early diagnosis improves the outcome.
CONCLUSION
Standardized treatment has yet to be developed. In our case, systemic corticosteroids were of limited value only.
背景
韦尔斯综合征是一种罕见的嗜酸性粒细胞谱系特发性皮肤病。诊断标准包括形态多样的皮肤疹伴嗜酸性粒细胞浸润、外周血嗜酸性粒细胞增多、病情复发缓解过程以及排除全身性疾病。诊断往往延迟。
病例介绍
我们报告一名28岁男性，近期出现瘙痒且有时疼痛的红斑。他的病史显示2012年11月开始出现夜间咳嗽，随后发展为全鼻窦炎。早期诊断可改善预后。
结论
尚未制定标准化治疗方案。在我们的病例中，全身用皮质类固醇仅具有有限价值。
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