Department of Neural and Behavioral Sciences, Penn State College of Medicine, Hershey, PA, USA.
Clinical Enteric Neuroscience Translational and Epidemiological Research (CENTER), Mayo Clinic, Rochester, MN, USA.
Nat Rev Gastroenterol Hepatol. 2020 Nov;17(11):673-685. doi: 10.1038/s41575-020-0339-z. Epub 2020 Jul 31.
The classic view portrays Parkinson disease (PD) as a motor disorder resulting from loss of substantia nigra pars compacta dopaminergic neurons. Multiple studies, however, describe prodromal, non-motor dysfunctions that affect the quality of life of patients who subsequently develop PD. These prodromal dysfunctions comprise a wide array of gastrointestinal motility disorders including dysphagia, delayed gastric emptying and chronic constipation. The histological hallmark of PD - misfolded α-synuclein aggregates that form Lewy bodies and neurites - is detected in the enteric nervous system prior to clinical diagnosis, suggesting that the gastrointestinal tract and its neural (vagal) connection to the central nervous system could have a major role in disease aetiology. This Review provides novel insights on the pathogenesis of PD, including gut-to-brain trafficking of α-synuclein as well as the newly discovered nigro-vagal pathway, and highlights how vagal connections from the gut could be the conduit by which ingested environmental pathogens enter the central nervous system and ultimately induce, or accelerate, PD progression. The pathogenic potential of various environmental neurotoxicants and the suitability and translational potential of experimental animal models of PD will be highlighted and appraised. Finally, the clinical manifestations of gastrointestinal involvement in PD and medications will be discussed briefly.
经典观点认为帕金森病 (PD) 是一种运动障碍,源于黑质致密部多巴胺能神经元的丧失。然而,多项研究描述了前驱期、非运动性功能障碍,这些障碍影响随后发展为 PD 的患者的生活质量。这些前驱期功能障碍包括广泛的胃肠道动力障碍,包括吞咽困难、胃排空延迟和慢性便秘。PD 的组织学标志——错误折叠的α-突触核蛋白聚集形成路易体和神经原纤维——在临床诊断前就已在肠神经系统中被检测到,这表明胃肠道及其与中枢神经系统的神经(迷走)连接可能在疾病发病机制中起主要作用。本综述提供了关于 PD 发病机制的新见解,包括α-突触核蛋白的肠-脑转运以及新发现的黑质迷走神经通路,并强调了肠道的迷走神经连接如何可能成为摄入的环境病原体进入中枢神经系统并最终诱导或加速 PD 进展的途径。将重点强调和评估各种环境神经毒素的致病潜力以及 PD 实验动物模型的适用性和转化潜力。最后,将简要讨论 PD 中胃肠道受累的临床表现和药物治疗。