Gori Tommaso
Kardiologie I and DZHK Standort Rhein-Main, Universitätsmedizin Mainz, 55131 Mainz, Germany.
Biomedicines. 2021 May 31;9(6):622. doi: 10.3390/biomedicines9060622.
The term coronary "artery vasculitis" is used for a diverse group of diseases with a wide spectrum of manifestations and severity. Clinical manifestations may include pericarditis or myocarditis due to involvement of the coronary microvasculature, stenosis, aneurysm, or spontaneous dissection of large coronaries, or vascular thrombosis. As compared to common atherosclerosis, patients with coronary artery vasculitis are younger and often have a more rapid disease progression. Several clinical entities have been associated with coronary artery vasculitis, including Kawasaki's disease, Takayasu's arteritis, polyarteritis nodosa, ANCA-associated vasculitis, giant-cell arteritis, and more recently a Kawasaki-like syndrome associated with SARS-COV-2 infection. This review will provide a short description of these conditions, their diagnosis and therapy for use by the practicing cardiologist.
术语“冠状动脉血管炎”用于描述一组表现形式和严重程度各异的疾病。临床表现可能包括由于冠状动脉微血管受累、狭窄、动脉瘤、大冠状动脉自发性夹层或血管血栓形成导致的心包炎或心肌炎。与常见的动脉粥样硬化相比,冠状动脉血管炎患者更年轻,且疾病进展通常更快。几种临床病症与冠状动脉血管炎相关,包括川崎病、高安动脉炎、结节性多动脉炎、抗中性粒细胞胞浆抗体相关性血管炎、巨细胞动脉炎,以及最近与SARS-CoV-2感染相关的川崎样综合征。本综述将简要描述这些病症、其诊断方法及治疗手段,供执业心脏病专家参考。