Hitaka Daisuke, Kono Tatsuo, Arai Junichi, Murakami Takashi, Takahashi-Igari Miho, Tagawa Manabu, Mori Kensaku, Takada Hidetoshi
Department of Pediatrics, University of Tsukuba Hospital.
Department of Neonatology, Ibaraki Children's Hospital, Ibaraki, Japan.
Radiol Case Rep. 2021 Aug 30;16(11):3374-3379. doi: 10.1016/j.radcr.2021.08.009. eCollection 2021 Nov.
A term male infant presented with congenital hepatic arterio-veno-portal shunts. A mass-like lesion in the left lobe of the liver received blood supply from not only the umbilical vein, but also the hepatic and inferior intrahepatic arteries, communicating with the hepatic and portal veins in a complicated manner, with an umbilical vein aneurysm. The blood flow of the arterio-veno-portal shunts spontaneously and gradually declined from the neonatal period to six years of age. Although mild high-output cardiac failure had developed, no life-threatening events or health problems originating from portosystemic shunts, such as pulmonary artery hypertension and hepatopulmonary syndrome, were observed. However, this report shows that scrupulous follow-up to identify pulmonary artery hypertension and hepatopulmonary syndrome should be continued because complete resolution of the arterio-veno-portal shunts was not obtained in this case.
一名足月男婴出现先天性肝动静脉门静脉分流。肝脏左叶的一个肿块样病变不仅接受来自脐静脉的血液供应，还接受肝动脉和肝内下动脉的血液供应，以复杂的方式与肝静脉和门静脉相通，并伴有脐静脉瘤。动静脉门静脉分流的血流从新生儿期到6岁时自发且逐渐减少。尽管已出现轻度高输出量心力衰竭，但未观察到源自门体分流的危及生命的事件或健康问题，如肺动脉高压和肝肺综合征。然而，本报告表明，由于该病例中动静脉门静脉分流未完全消失，应继续进行仔细随访以识别肺动脉高压和肝肺综合征。
