Center for Molecular Cardiology, University of Zurich, Wagistrasse 12, 8952 Schlieren, Switzerland.
University Heart Center, Department of Cardiology, University Hospital, Rämistrasse 100, 8091 Zurich, Switzerland.
Eur Heart J. 2022 Feb 12;43(7):683-697. doi: 10.1093/eurheartj/ehab757.
Calcific aortic valve disease (CAVD) is a highly prevalent condition that comprises a disease continuum, ranging from microscopic changes to profound fibro-calcific leaflet remodelling, culminating in aortic stenosis, heart failure, and ultimately premature death. Traditional risk factors, such as hypercholesterolaemia and (systolic) hypertension, are shared among atherosclerotic cardiovascular disease and CAVD, yet the molecular and cellular mechanisms differ markedly. Statin-induced low-density lipoprotein cholesterol lowering, a remedy highly effective for secondary prevention of atherosclerotic cardiovascular disease, consistently failed to impact CAVD progression or to improve patient outcomes. However, recently completed phase II trials provide hope that pharmaceutical tactics directed at other targets implicated in CAVD pathogenesis offer an avenue to alter the course of the disease non-invasively. Herein, we delineate key players of CAVD pathobiology, outline mechanisms that entail compromised endothelial barrier function, and promote lipid homing, immune-cell infiltration, and deranged phospho-calcium metabolism that collectively perpetuate a pro-inflammatory/pro-osteogenic milieu in which valvular interstitial cells increasingly adopt myofibro-/osteoblast-like properties, thereby fostering fibro-calcific leaflet remodelling and eventually resulting in left ventricular outflow obstruction. We provide a glimpse into the most promising targets on the horizon, including lipoprotein(a), mineral-binding matrix Gla protein, soluble guanylate cyclase, dipeptidyl peptidase-4 as well as candidates involved in regulating phospho-calcium metabolism and valvular angiotensin II synthesis and ultimately discuss their potential for a future therapy of this insidious disease.
钙化性主动脉瓣疾病 (CAVD) 是一种高发疾病,它包含一个疾病连续体,从微观变化到严重的纤维-钙化瓣叶重塑,最终导致主动脉瓣狭窄、心力衰竭,最终导致过早死亡。传统的风险因素,如高胆固醇血症和(收缩压)高血压,在动脉粥样硬化性心血管疾病和 CAVD 中都有共同之处,但分子和细胞机制却有明显的不同。他汀类药物降低低密度脂蛋白胆固醇,这是一种非常有效的二级预防动脉粥样硬化性心血管疾病的方法,但它始终未能影响 CAVD 的进展或改善患者的预后。然而,最近完成的 II 期临床试验提供了希望,即针对 CAVD 发病机制中其他靶点的药物治疗策略提供了一条非侵入性改变疾病进程的途径。在此,我们阐述了 CAVD 病理生物学的关键因素,概述了涉及内皮屏障功能受损的机制,并促进了脂质归巢、免疫细胞浸润和紊乱的磷钙代谢,这些机制共同维持了一个促炎/促成骨的环境,其中瓣膜间质细胞越来越多地采用成纤维细胞/成骨细胞样特性,从而促进纤维-钙化瓣叶重塑,最终导致左心室流出道梗阻。我们展望了最有前途的靶点,包括脂蛋白 (a)、结合矿物质的基质 Gla 蛋白、可溶性鸟苷酸环化酶、二肽基肽酶-4 以及参与调节磷钙代谢和瓣膜血管紧张素 II 合成的候选药物,并最终讨论了它们在这种隐匿性疾病治疗中的潜在应用。