Kagawa Y, Kashihara S, Kuramoto S, Maetani S
Gastroenterology. 1978 Jun;74(6):1286-94.
A case of carcinoma arising in a congenitally dilated biliary tract is reported. Forty-seven cases in which congenital dilatation of the biliary tract was associated with carcinoma were found in the world literature and analyzed. The association of carcinoma with congenital biliary ductal dilatation was found to be higher than previously recognized. Carcinoma may arise in any cystic portion, extrahepatic or intrahepatic. If technically safe and feasible, primary excision of the choledochal cyst is advisable, to prevent the risk of later malignant change in the unexcised cyst.
本文报道了一例发生于先天性扩张胆管的癌。在世界文献中发现并分析了47例胆管先天性扩张合并癌的病例。结果发现，癌与先天性胆管扩张的关联比之前认为的更高。癌可发生于任何肝外或肝内的囊性部位。如果技术上安全可行，建议对胆总管囊肿进行一期切除，以防止未切除囊肿日后发生恶变的风险。
